An unusual case of acquired generalized lipodystrophy (panniculitis variety)

Acquired generalized lipodystrophy (AGL) is a rare disease characterized by variable loss of adipose tissue and concurrent metabolic derangements, typically with childhood or adolescent onset. AGL has three subclassifications: panniculitis (type 1), autoimmune disease (type 2), and idiopathic (type...

Full description

Saved in:
Bibliographic Details
Published in:Pediatric dermatology 2024-11, Vol.41 (6), p.1152-1155
Main Authors: Hill, Marlee, Weissman, Amanda S., Hirshburg, Jason, McBride, Jeffrey D., Lawrence, Hillary
Format: Article
Language:English
Subjects:
acquired generalized
Adipose tissue
Autoimmune diseases
Child, Preschool
Children
Female
Humans
Lipoatrophy
Lipodystrophy
Lipodystrophy - diagnosis
Lipodystrophy - pathology
panniculitis
Panniculitis - diagnosis
Panniculitis - etiology
Panniculitis - pathology
pediatric dermatology
Citations: Items that this one cites
Online Access:Get full text
Tags: Add Tag
No Tags, Be the first to tag this record!
Description
Summary:Acquired generalized lipodystrophy (AGL) is a rare disease characterized by variable loss of adipose tissue and concurrent metabolic derangements, typically with childhood or adolescent onset. AGL has three subclassifications: panniculitis (type 1), autoimmune disease (type 2), and idiopathic (type 3). This report highlights a rare case of AGL type 1 in a previously healthy 3‐year‐old female who presented with diffuse erythematous subcutaneous nodules, progressive lipoatrophy, and histopathological findings of a lobular panniculitis.
ISSN:0736-8046
1525-1470
1525-1470
DOI:10.1111/pde.15668