Malignant Nerve Sheath Tumour – A Case Report

Malignant nerve sheath tumors are rare and aggressive soft tissue sarcomas. They contribute to 5–10% of all soft tissue sarcomas. They can be sporadic, occur in patients with NF1 (neurofibromatosis 1) or can occur after radiation therapy. A high rate of recurrence and hematogenous metastasis is seen...

Full description

Saved in:
Bibliographic Details
Published in:Indian journal of otolaryngology, and head, and neck surgery and head, and neck surgery, 2024-08, Vol.76 (4), p.3511-3518
Main Authors: Majitha, C.S., Pillai, Suresh, Shetty, Shama, Pujary, Kailesh, Menon, Girish
Format: Article
Language:English
Subjects:
Clinical Report
Head and Neck Surgery
Medicine
Medicine & Public Health
Otorhinolaryngology
Citations: Items that this one cites
Online Access:Get full text
Tags: Add Tag
No Tags, Be the first to tag this record!
Description
Summary:Malignant nerve sheath tumors are rare and aggressive soft tissue sarcomas. They contribute to 5–10% of all soft tissue sarcomas. They can be sporadic, occur in patients with NF1 (neurofibromatosis 1) or can occur after radiation therapy. A high rate of recurrence and hematogenous metastasis is seen in these patients. They are also associated with poor prognosis. A case of malignant nerve sheath tumor seen in a 44-year-old male with pre-existing NF1 is being discussed here due to the unique nature of the disease and its rarity.
ISSN:2231-3796
0973-7707
DOI:10.1007/s12070-024-04591-1