Malignant peripheral nerve sheath tumor arising from an adrenal ganglioneuroma in a 6-year-old boy

This report describes the youngest patient to develop a malignant peripheral nerve sheath tumor arising from a ganglioneuroma (MPNST ex Ganglioneuroma). The patient, a 6-year-old boy, was never irradiated and had no history or stigmata of neurofibromatosis. The report also includes a review of the p...

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Bibliographic Details
Published in:Pediatric and developmental pathology 2004-05, Vol.7 (3), p.277-284
Main Authors: de Chadarévian, Jean-Pierre, MaePascasio, Judy, Halligan, Gregory E, Katz, Douglas A, Locono, Joseph A, Kimmel, Stephen, Katsetos, Christos D
Format: Article
Language:English
Subjects:
Adrenal Gland Neoplasms - pathology
Adrenal Gland Neoplasms - therapy
Adrenal Gland Neoplasms - urine
Adrenalectomy
Antineoplastic Combined Chemotherapy Protocols
Child
Ganglioneuroma - pathology
Ganglioneuroma - therapy
Ganglioneuroma - urine
Homovanillic Acid - urine
Humans
Male
Nerve Sheath Neoplasms - pathology
Nerve Sheath Neoplasms - therapy
Nerve Sheath Neoplasms - urine
Vanilmandelic Acid - urine
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Summary:This report describes the youngest patient to develop a malignant peripheral nerve sheath tumor arising from a ganglioneuroma (MPNST ex Ganglioneuroma). The patient, a 6-year-old boy, was never irradiated and had no history or stigmata of neurofibromatosis. The report also includes a review of the previously published related cases, and an analysis of the immunohistochemistry and electron microscopy data available to date on the subject.
ISSN:1093-5266
1615-5742
DOI:10.1007/s10024-004-8084-9