Hypersensitive Carotid Sinus Syndrome Due to Neurofibromatosis‐1 and Manifested by Repeated Episodes of Syncope

A 28‐year‐old patient with neurofibromatosis‐1 presented with syncope. The exam demonstrated a mass adjacent and inferior to the right occiput that extended to the posterior lateral right‐sided neck. Initial invasive and noninvasive testing was negative. Imaging of her head and neck demonstrated a l...

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Bibliographic Details
Published in:Pacing and clinical electrophysiology 2004-11, Vol.27 (11), p.1571-1573
Main Authors: SUTHERLAND, JESSICA A., STOBIE, PAUL, SWARUP, VIJAY, TIERNEY, SEAN P., LIN, ALBERT C., BURKE, MARTIN C.
Format: Article
Language:English
Subjects:
Adult
Carotid Sinus - physiopathology
Carotid Stenosis - etiology
Defibrillators, Implantable
Female
Follow-Up Studies
Head and Neck Neoplasms - complications
Humans
hypersensitive carotid sinus
Neurofibromatosis 1 - complications
neurofibromatosis‐1
syncope
Syncope - etiology
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Description
Summary:A 28‐year‐old patient with neurofibromatosis‐1 presented with syncope. The exam demonstrated a mass adjacent and inferior to the right occiput that extended to the posterior lateral right‐sided neck. Initial invasive and noninvasive testing was negative. Imaging of her head and neck demonstrated a large neurofibroma enveloping her right carotid sinus without vessel occlusion or evidence of malignancy. An event recorder documented asystole. A pacemaker was implanted to avoid the surgical morbidity of removing the neck mass. The patient has since been free of syncope. We believe neurofibromatosis‐1 should be included in the differential of syncope.
ISSN:0147-8389
1540-8159
DOI:10.1111/j.1540-8159.2004.00680.x