An Unusual Case of Congenital Linear Eccrine Spiradenoma

• Published in: Pediatric dermatology 2009-03, Vol.26 (2), p.180-183
• Main Authors: Rodríguez‐Martín, Marina, Sánchez González, Rosalba, Sáez‐Rodríguez, Miguel, García‐Bustínduy, M., Martín‐Herrera, Antonio, Noda‐Cabrera, Antonio
• Format: Article
• Language: English
• Subjects: Adenoma, Sweat Gland - congenital; Adenoma, Sweat Gland - pathology; Biological and medical sciences; Child; Dermatology; Eccrine Glands - pathology; Female; Humans; Medical sciences; Neoplasms, Multiple Primary - congenital; Neoplasms, Multiple Primary - pathology; Skin involvement in other diseases. Miscellaneous. General aspects; Sweat Gland Neoplasms - congenital; Sweat Gland Neoplasms - pathology; Tumors of the skin and soft tissue. Premalignant lesions
• ISSN: 0736-8046; 1525-1470
• DOI: 10.1111/j.1525-1470.2009.00879.x

:  Eccrine spiradenoma (ES) is a benign uncommon tumor of skin adnexa with a characteristic clinical and histopathological presentation. Typically, it presents as a painful, slow growing and solitary nodule on the head or upper trunk in adult patients. We report a child with linear ES which presented with asymptomatic papulonodular lesions in a blaschkoid distribution on the face. Cases reported in the literature of multiple spiradenomas are very rare and multiple linear lesions are even rarer. To date, 21 cases of linear/multiple ES have been reported. Of these, eight were in children or adolescents. We report an additional case of this rare clinical presentation and review the literature.