Purely cutaneous Rosai-Dorfman disease

Sinus histiocytosis with massive lymphadenopathy or Rosai-Dorfman disease is a non-Langerhans cell histiocytosis of unknown etiolosy. The most characteristic feature is lymphadenopathy, especially that of cervical lymph nodes. In approximately 40% of patients there are extranodal manifestations of t...

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Bibliographic Details
Published in:Hautarzt 2004-10, Vol.55 (10), p.969-971
Main Authors: Plettenberg, H, Artik, S, Kuhn, A, Megahed, M, Ruzicka, T, Kruse, R
Format: Article
Language:ger
Subjects:
Aged
Biopsy
Diagnosis, Differential
Female
Histiocytosis, Sinus - diagnosis
Histiocytosis, Sinus - drug therapy
Histiocytosis, Sinus - pathology
Humans
Methylprednisolone - therapeutic use
Recurrence
Skin - pathology
Skin Diseases - diagnosis
Skin Diseases - drug therapy
Skin Diseases - pathology
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Summary:Sinus histiocytosis with massive lymphadenopathy or Rosai-Dorfman disease is a non-Langerhans cell histiocytosis of unknown etiolosy. The most characteristic feature is lymphadenopathy, especially that of cervical lymph nodes. In approximately 40% of patients there are extranodal manifestations of the disease. Skin is the most commonly affected organ (27%). We report a 79-year-old female patient with purely cutaneous manifestations. This form of the disease is a very rare differential diagnosis in dermatology.
ISSN:0017-8470