Fibrolipomatous hamartoma in a patient with tuberous sclerosis: Report of a case

Tuberous sclerosis is a rare congenital disorder with an incidence of 1 in 6000 births. The classic triad is seizure, mental deficiency, and angiofibromas. Orofacial manifestations include fibrous hyperplasia, hemangioma, bifid uvula, cleft lip and palate, macroglossia, high arched palate, and ename...

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Published in:Oral surgery, oral medicine, oral pathology, oral radiology and endodontics oral medicine, oral pathology, oral radiology and endodontics, 2005-02, Vol.99 (2), p.202-206
Main Authors: Çelenk, Peruze, Alkan, Alper, Canger, E. Murat, Günhan, Ömer
Format: Article
Language:English
Subjects:
Adipocytes - pathology
Adolescent
Biological and medical sciences
Calcinosis - pathology
Collagen
Curettage
Dentistry
Hamartoma - complications
Hamartoma - pathology
Humans
Male
Mandibular Diseases - complications
Mandibular Diseases - pathology
Medical sciences
Neurology
Otorhinolaryngology. Stomatology
Tomography, X-Ray Computed
Tuberous Sclerosis - complications
Tumors of the nervous system. Phacomatoses
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Summary:Tuberous sclerosis is a rare congenital disorder with an incidence of 1 in 6000 births. The classic triad is seizure, mental deficiency, and angiofibromas. Orofacial manifestations include fibrous hyperplasia, hemangioma, bifid uvula, cleft lip and palate, macroglossia, high arched palate, and enamel defects. Benign tumors of the jaws including desmoplastic fibroma, calcifying odontogenic tumor, and odontogenic myxoma have been recently reported in tuberous sclerosis. This case report adds fibrolipomatous hamartoma of the mandible to this list.
ISSN:1079-2104
1528-395X
DOI:10.1016/j.tripleo.2004.07.003