Peliosis hepatis causing inferior vena cava compression in a 3-year-old child

Peliosis hepatis is a rare benign condition characterized by oval or irregular, multiple blood-filled spaces within the liver parenchyma. It is most commonly seen in adults and may be idiopathic, but has various associations including malignancy, infection and drugs. The imaging findings are often n...

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Bibliographic Details
Published in:Pediatric radiology 2005-02, Vol.35 (2), p.209-211
Main Authors: Hiorns, Melanie P, Rossi, Umberto G, Roebuck, Derek J
Format: Article
Language:English
Subjects:
Child, Preschool
Constriction, Pathologic - etiology
Female
Humans
Peliosis Hepatis - diagnosis
Tomography, X-Ray Computed
Vena Cava, Inferior - pathology
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Summary:Peliosis hepatis is a rare benign condition characterized by oval or irregular, multiple blood-filled spaces within the liver parenchyma. It is most commonly seen in adults and may be idiopathic, but has various associations including malignancy, infection and drugs. The imaging findings are often non-specific and the condition may be mistaken for multiple abscesses, metastases or vascular malformations. Peliosis hepatis is an especially rare condition in children and to our knowledge only six cases have been described in the literature. Our case describes and illustrates peliosis in a 3-year-old girl and is the first described in any age group to cause complete IVC obstruction. The patient subsequently made a full recovery.
ISSN:0301-0449
1432-1998
DOI:10.1007/s00247-004-1311-8