Severe stenosis of a long tracheal segment, with agenesis of the right lung and left pulmonary arterial sling

A baby presented at term with respiratory distress was managed with extracorporeal membrane oxygenation. Bronchoscopy revealed tracheal hypoplasia, complete tracheal rings, and agenesis of the right main bronchus. Echocardiography showed a left pulmonary arterial sling arising from the proximal part...

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Bibliographic Details
Published in:Cardiology in the young 2006-02, Vol.16 (1), p.89-91
Main Authors: Munro, Hamish M., Sorbello, Andrea M. C., Nykanen, David G.
Format: Article
Language:English
Subjects:
Abnormalities, Multiple - diagnosis
Angiography
Brief Report
Bronchoscopy
Congenital heart disease
Diagnosis, Differential
Echocardiography
Fatal Outcome
Female
great vessel anomalies
Humans
Infant, Newborn
lung
Lung - abnormalities
Lungs
Medical imaging
Pulmonary arteries
Pulmonary Artery - abnormalities
Tracheal Stenosis - diagnosis
Veins & arteries
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Summary:A baby presented at term with respiratory distress was managed with extracorporeal membrane oxygenation. Bronchoscopy revealed tracheal hypoplasia, complete tracheal rings, and agenesis of the right main bronchus. Echocardiography showed a left pulmonary arterial sling arising from the proximal part of the right pulmonary artery. Cardiac catheterization demonstrated abnormal pulmonary vasculature in the left lung which would have prevented survival, even after surgical repair. Diagnostic catheterization was important in delineating the anatomy, and aided in the decision not to proceed with surgical repair.
ISSN:1047-9511
1467-1107
DOI:10.1017/S1047951105002179