Dental findings and rehabilitation in familial osteodysplasia (Anderson type): a case report

Familial osteodysplasia is a disorder of osteogenesis with an autosomal recessive pattern of inheritance which predominantly affects facial bones. No recent case had been reported, particularly from a dental point of view since the syndrome was first described by Anderson et al (JAMA 1972;220:1687–9...

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Bibliographic Details
Published in:Oral diseases 2006-03, Vol.12 (2), p.208-212
Main Authors: Deger, S, Tabar, G, Sermet, B, Tanyeri, H, Kurklu, E
Format: Article
Language:English
Subjects:
Adult
Bone Diseases, Developmental - genetics
conus crown
Crowns
Dental Abutments
Dentistry
Denture Design
Denture, Overlay
Denture, Partial, Removable
familial osteodysplasia
Humans
Male
Malocclusion - genetics
Mandible - abnormalities
mandibular fracture
Mouth Rehabilitation
Tooth Abnormalities - genetics
Tooth Crown - abnormalities
Tooth Root - abnormalities
Tooth, Impacted - genetics
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Summary:Familial osteodysplasia is a disorder of osteogenesis with an autosomal recessive pattern of inheritance which predominantly affects facial bones. No recent case had been reported, particularly from a dental point of view since the syndrome was first described by Anderson et al (JAMA 1972;220:1687–93). A 23‐year‐old male with familial osteodysplasia was presented in maxillofacial and dental aspects with clinical and radiological manifestations including malocclusion, abnormal teeth alignment, impacted teeth, shape disturbances including uncompleted coronal formation, root shortening with bulbous form, high angled mandible and elongation of the corpus of mandible. Recognation of the syndromal features prior to any dental intervention is of paramount importance because of increased inclination to spontaneous mandibular fractures. Hence, no surgical intervention was performed for impacted teeth. Following the extractions of severely mobile teeth, a definitive restoration was fabricated as distal‐extension removable partial dentures with conus crown telescopic system. The aesthetic and functional outcome was satisfactory for the patient. In conclusion, dentists appear to play an important role in the recognition of familial osteodysplasia, based on maxillofacial and dentoalveolar findings. Awareness of the syndromal features, especially of spontaneous fractures, would detect the limitations for dental interventions and treatment planning.
ISSN:1354-523X
1601-0825
DOI:10.1111/j.1601-0825.2005.01178.x