Ectodermal Dysplasia: Retrospective Study of Fifteen Cases

The aim of this article is to review possible cranio-maxillofacial deformative consequences associated with hypohidrotic ectodermal dysplasia and embryonic malformations, which include dental ageneses, and describe the oral habilitation. Hypohidrotic ectodermal dysplasia patients had a clinical exam...

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Bibliographic Details
Published in:Archives of medical research 2006-04, Vol.37 (3), p.403-409
Main Authors: Yavuz, Izzet, Baskan, Zelal, Ulku, Refik, Dulgergil, Turksel Coruh, Dari, Osman, Ece, Aydin, Yavuz, Yasemin, Dari, Kadriye Oya
Format: Article
Language:English
Subjects:
Adolescent
Adult
Cephalometry
Child
Child, Preschool
Denture
Ectodermal Dysplasia - complications
Ectodermal Dysplasia - diagnostic imaging
Ectodermal Dysplasia - pathology
Female
Humans
Hypohidrotic ectodermal dysplasias
Male
Middle Aged
Nails - pathology
Pedigree
Radiography
Retrospective Studies
Skin - pathology
Tooth - diagnostic imaging
Tooth - pathology
Tooth ageneses
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Summary:The aim of this article is to review possible cranio-maxillofacial deformative consequences associated with hypohidrotic ectodermal dysplasia and embryonic malformations, which include dental ageneses, and describe the oral habilitation. Hypohidrotic ectodermal dysplasia patients had a clinical examination and underwent radiographic and Steiner's analyses and a respiratory capability test before assessment and treatment. Fifteen patients (eight males and seven females, aged 5–45 years) had tooth ageneses (from hypodontia to anodontia) associated with cutaneous dyshydrosis and hair and nail dystrophy. Most patients had sparse or absent hair, a short face with an unusual facial concavity, a maxillary retrusion and a relative mandibular protrusion. Dentists must conduct a comprehensive and multidisciplinary approach to these patients in order to improve their dental, masticatory, growth and orthognathic conditions.
ISSN:0188-4409
1873-5487
DOI:10.1016/j.arcmed.2005.06.016