Renal calculi in a patient with Erdheim-Chester disease

Erdheim-Chester Disease (ECD) is a non-inherited multifocal lipid storing histiocytosis. It is a rare disease characterised by lipid-laden monocyte infiltration of long bones causing cortical sclerosis and characteristic X-ray appearances. It also involves extraskeletal tissue in up to 50% of cases...

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Bibliographic Details
Published in:International urology and nephrology 2005-09, Vol.37 (3), p.453-456
Main Authors: Dundee, Philip, Bouchier-Hayes, David, Iles, Linda, Costello, Anthony
Format: Article
Language:English
Subjects:
Erdheim-Chester Disease - complications
Erdheim-Chester Disease - pathology
Humans
Hydronephrosis - etiology
Male
Middle Aged
Ureteral Calculi - etiology
Ureteral Calculi - pathology
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Summary:Erdheim-Chester Disease (ECD) is a non-inherited multifocal lipid storing histiocytosis. It is a rare disease characterised by lipid-laden monocyte infiltration of long bones causing cortical sclerosis and characteristic X-ray appearances. It also involves extraskeletal tissue in up to 50% of cases including retroperitoneal and renal infiltration. We report a patient with long standing ECD with widespread extraskeletal involvement, including significant renal infiltration, presenting with left hydronephrosis secondery obstruction from a proximal ureteric calculas.
ISSN:0301-1623
1573-2584
DOI:10.1007/s11255-004-0020-4