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Endovascular Repair of Dissecting Thoracic Aortic Aneurysm in a Patient with Turner Syndrome
Purpose: To report a rare case of dissecting thoracic aortic aneurysm in a young patient with Turner syndrome owing to complete or partial monosomy of the X chromosome. Case Report: A 22-year-old patient with Turner syndrome presented with a 2-month history of voice loss and dysphagia. Multislice co...
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| Published in: | Journal of endovascular therapy 2006-10, Vol.13 (5), p.693-696 |
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| Main Authors: | , , , , , , , , , |
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| cited_by | cdi_FETCH-LOGICAL-c341t-3f6ab80f70f74b553319b4e5ae3885700034cc96cc456420be977559d00fde433 |
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| cites | cdi_FETCH-LOGICAL-c341t-3f6ab80f70f74b553319b4e5ae3885700034cc96cc456420be977559d00fde433 |
| container_end_page | 696 |
| container_issue | 5 |
| container_start_page | 693 |
| container_title | Journal of endovascular therapy |
| container_volume | 13 |
| creator | Petrov, Ivo Nedevska, Maria Chilingirova, Nezabravka Simeonov, Peyo Kratunkov, Pencho Stoinova, Vesela Nikolov, Dimitar Konteva, Mariana Tzarianski, Georgi Tschirkov, Alexander I. |
| description | Purpose:
To report a rare case of dissecting thoracic aortic aneurysm in a young patient with Turner syndrome owing to complete or partial monosomy of the X chromosome.
Case Report:
A 22-year-old patient with Turner syndrome presented with a 2-month history of voice loss and dysphagia. Multislice computed tomography (MSCT) disclosed a large (53times75-mm) aneurysm with focal dissection affecting the distal part of the aortic arch and the proximal descending aorta, partially involving the left subclavian artery. A TAG endoprosthesis was implanted without complications. MSCT scans at 3 and 6 months after the procedure showed good position and patency of the stent-graft, with total exclusion and shrinkage of the aneurysm. After 1 year of follow-up, she is doing well, without voice disturbances or dysphagia.
Conclusion:
Although cardiovascular malformations are common in patients with Turner syndrome, dissecting thoracic aortic aneurysm is unusual. Stent-graft repair would appear to be feasible in this situation, but long-term implantation in young patients has not been explored. |
| doi_str_mv | 10.1583/05-1663.1 |
| format | article |
| fullrecord | <record><control><sourceid>proquest_cross</sourceid><recordid>TN_cdi_proquest_miscellaneous_68955208</recordid><sourceformat>XML</sourceformat><sourcesystem>PC</sourcesystem><sage_id>10.1583_05-1663.1</sage_id><sourcerecordid>1156279751</sourcerecordid><originalsourceid>FETCH-LOGICAL-c341t-3f6ab80f70f74b553319b4e5ae3885700034cc96cc456420be977559d00fde433</originalsourceid><addsrcrecordid>eNplkFtr3DAQhUVpaC7tQ_9AEH0I5MHpyNLI9mPIpQ0EEtrtW0HI8nhXYW1tJLth_31ssrDQwMCZgY8zh8PYVwEXAkv5HTATWssL8YEdCVTThQgf5z3XmYa8PGTHKT0B5CIX4hM7FAWoXCMesb83fRP-2eTGtY38F22sjzy0_NqnRG7w_ZIvViFa5x2_DHGYpacxblPHfc8tf7SDp37gL35Y8cUYe4r897ZvYujoMzto7TrRl52esD-3N4urn9n9w4-7q8v7zEklhky22tYltMU0qkaUUlS1IrQkyxILAJDKuUo7p1CrHGqqigKxagDahpSUJ-zszXcTw_NIaTCdT47Wa9tTGJPRZYWYQzmB3_4Dn8IUecpmpmIEVAXObudvkIshpUit2UTf2bg1AszctwE0c99GTOzpznCsO2r25K7gfbRkl7T_9t7pFaIxhKY</addsrcrecordid><sourcetype>Aggregation Database</sourcetype><iscdi>true</iscdi><recordtype>article</recordtype><pqid>211109753</pqid></control><display><type>article</type><title>Endovascular Repair of Dissecting Thoracic Aortic Aneurysm in a Patient with Turner Syndrome</title><source>Sage Journals Online</source><creator>Petrov, Ivo ; Nedevska, Maria ; Chilingirova, Nezabravka ; Simeonov, Peyo ; Kratunkov, Pencho ; Stoinova, Vesela ; Nikolov, Dimitar ; Konteva, Mariana ; Tzarianski, Georgi ; Tschirkov, Alexander I.</creator><creatorcontrib>Petrov, Ivo ; Nedevska, Maria ; Chilingirova, Nezabravka ; Simeonov, Peyo ; Kratunkov, Pencho ; Stoinova, Vesela ; Nikolov, Dimitar ; Konteva, Mariana ; Tzarianski, Georgi ; Tschirkov, Alexander I.</creatorcontrib><description>Purpose:
To report a rare case of dissecting thoracic aortic aneurysm in a young patient with Turner syndrome owing to complete or partial monosomy of the X chromosome.
Case Report:
A 22-year-old patient with Turner syndrome presented with a 2-month history of voice loss and dysphagia. Multislice computed tomography (MSCT) disclosed a large (53times75-mm) aneurysm with focal dissection affecting the distal part of the aortic arch and the proximal descending aorta, partially involving the left subclavian artery. A TAG endoprosthesis was implanted without complications. MSCT scans at 3 and 6 months after the procedure showed good position and patency of the stent-graft, with total exclusion and shrinkage of the aneurysm. After 1 year of follow-up, she is doing well, without voice disturbances or dysphagia.
Conclusion:
Although cardiovascular malformations are common in patients with Turner syndrome, dissecting thoracic aortic aneurysm is unusual. Stent-graft repair would appear to be feasible in this situation, but long-term implantation in young patients has not been explored.</description><identifier>ISSN: 1526-6028</identifier><identifier>EISSN: 1545-1550</identifier><identifier>DOI: 10.1583/05-1663.1</identifier><identifier>PMID: 17042655</identifier><language>eng</language><publisher>Los Angeles, CA: SAGE Publications</publisher><subject>Adult ; Aneurysm, Dissecting - diagnostic imaging ; Aneurysm, Dissecting - etiology ; Aneurysm, Dissecting - surgery ; Aneurysms ; Aortic Aneurysm, Thoracic - diagnostic imaging ; Aortic Aneurysm, Thoracic - etiology ; Aortic Aneurysm, Thoracic - surgery ; Blood Vessel Prosthesis Implantation ; Case studies ; Female ; Genetic disorders ; Humans ; Hypothyroidism ; Medical treatment ; Patients ; Risk factors ; Stents ; Subclavian Artery - surgery ; Tomography, X-Ray Computed ; Turner Syndrome - complications ; Turner Syndrome - diagnostic imaging ; Vascular Patency ; Vascular surgery ; Veins & arteries</subject><ispartof>Journal of endovascular therapy, 2006-10, Vol.13 (5), p.693-696</ispartof><rights>2006 SAGE Publications</rights><rights>Copyright Alliance Communications Group, A Division of Allen Press, Inc. Oct 2006</rights><lds50>peer_reviewed</lds50><woscitedreferencessubscribed>false</woscitedreferencessubscribed><citedby>FETCH-LOGICAL-c341t-3f6ab80f70f74b553319b4e5ae3885700034cc96cc456420be977559d00fde433</citedby><cites>FETCH-LOGICAL-c341t-3f6ab80f70f74b553319b4e5ae3885700034cc96cc456420be977559d00fde433</cites></display><links><openurl>$$Topenurl_article</openurl><openurlfulltext>$$Topenurlfull_article</openurlfulltext><thumbnail>$$Tsyndetics_thumb_exl</thumbnail><link.rule.ids>314,780,784,27924,27925,79364</link.rule.ids><backlink>$$Uhttps://www.ncbi.nlm.nih.gov/pubmed/17042655$$D View this record in MEDLINE/PubMed$$Hfree_for_read</backlink></links><search><creatorcontrib>Petrov, Ivo</creatorcontrib><creatorcontrib>Nedevska, Maria</creatorcontrib><creatorcontrib>Chilingirova, Nezabravka</creatorcontrib><creatorcontrib>Simeonov, Peyo</creatorcontrib><creatorcontrib>Kratunkov, Pencho</creatorcontrib><creatorcontrib>Stoinova, Vesela</creatorcontrib><creatorcontrib>Nikolov, Dimitar</creatorcontrib><creatorcontrib>Konteva, Mariana</creatorcontrib><creatorcontrib>Tzarianski, Georgi</creatorcontrib><creatorcontrib>Tschirkov, Alexander I.</creatorcontrib><title>Endovascular Repair of Dissecting Thoracic Aortic Aneurysm in a Patient with Turner Syndrome</title><title>Journal of endovascular therapy</title><addtitle>J Endovasc Ther</addtitle><description>Purpose:
To report a rare case of dissecting thoracic aortic aneurysm in a young patient with Turner syndrome owing to complete or partial monosomy of the X chromosome.
Case Report:
A 22-year-old patient with Turner syndrome presented with a 2-month history of voice loss and dysphagia. Multislice computed tomography (MSCT) disclosed a large (53times75-mm) aneurysm with focal dissection affecting the distal part of the aortic arch and the proximal descending aorta, partially involving the left subclavian artery. A TAG endoprosthesis was implanted without complications. MSCT scans at 3 and 6 months after the procedure showed good position and patency of the stent-graft, with total exclusion and shrinkage of the aneurysm. After 1 year of follow-up, she is doing well, without voice disturbances or dysphagia.
Conclusion:
Although cardiovascular malformations are common in patients with Turner syndrome, dissecting thoracic aortic aneurysm is unusual. Stent-graft repair would appear to be feasible in this situation, but long-term implantation in young patients has not been explored.</description><subject>Adult</subject><subject>Aneurysm, Dissecting - diagnostic imaging</subject><subject>Aneurysm, Dissecting - etiology</subject><subject>Aneurysm, Dissecting - surgery</subject><subject>Aneurysms</subject><subject>Aortic Aneurysm, Thoracic - diagnostic imaging</subject><subject>Aortic Aneurysm, Thoracic - etiology</subject><subject>Aortic Aneurysm, Thoracic - surgery</subject><subject>Blood Vessel Prosthesis Implantation</subject><subject>Case studies</subject><subject>Female</subject><subject>Genetic disorders</subject><subject>Humans</subject><subject>Hypothyroidism</subject><subject>Medical treatment</subject><subject>Patients</subject><subject>Risk factors</subject><subject>Stents</subject><subject>Subclavian Artery - surgery</subject><subject>Tomography, X-Ray Computed</subject><subject>Turner Syndrome - complications</subject><subject>Turner Syndrome - diagnostic imaging</subject><subject>Vascular Patency</subject><subject>Vascular surgery</subject><subject>Veins & arteries</subject><issn>1526-6028</issn><issn>1545-1550</issn><fulltext>true</fulltext><rsrctype>article</rsrctype><creationdate>2006</creationdate><recordtype>article</recordtype><recordid>eNplkFtr3DAQhUVpaC7tQ_9AEH0I5MHpyNLI9mPIpQ0EEtrtW0HI8nhXYW1tJLth_31ssrDQwMCZgY8zh8PYVwEXAkv5HTATWssL8YEdCVTThQgf5z3XmYa8PGTHKT0B5CIX4hM7FAWoXCMesb83fRP-2eTGtY38F22sjzy0_NqnRG7w_ZIvViFa5x2_DHGYpacxblPHfc8tf7SDp37gL35Y8cUYe4r897ZvYujoMzto7TrRl52esD-3N4urn9n9w4-7q8v7zEklhky22tYltMU0qkaUUlS1IrQkyxILAJDKuUo7p1CrHGqqigKxagDahpSUJ-zszXcTw_NIaTCdT47Wa9tTGJPRZYWYQzmB3_4Dn8IUecpmpmIEVAXObudvkIshpUit2UTf2bg1AszctwE0c99GTOzpznCsO2r25K7gfbRkl7T_9t7pFaIxhKY</recordid><startdate>200610</startdate><enddate>200610</enddate><creator>Petrov, Ivo</creator><creator>Nedevska, Maria</creator><creator>Chilingirova, Nezabravka</creator><creator>Simeonov, Peyo</creator><creator>Kratunkov, Pencho</creator><creator>Stoinova, Vesela</creator><creator>Nikolov, Dimitar</creator><creator>Konteva, Mariana</creator><creator>Tzarianski, Georgi</creator><creator>Tschirkov, Alexander I.</creator><general>SAGE Publications</general><general>Allen Press Inc</general><scope>CGR</scope><scope>CUY</scope><scope>CVF</scope><scope>ECM</scope><scope>EIF</scope><scope>NPM</scope><scope>AAYXX</scope><scope>CITATION</scope><scope>3V.</scope><scope>7RV</scope><scope>7X7</scope><scope>7XB</scope><scope>88E</scope><scope>8FI</scope><scope>8FJ</scope><scope>8FK</scope><scope>ABUWG</scope><scope>AFKRA</scope><scope>BENPR</scope><scope>CCPQU</scope><scope>FYUFA</scope><scope>GHDGH</scope><scope>K9.</scope><scope>KB0</scope><scope>M0S</scope><scope>M1P</scope><scope>NAPCQ</scope><scope>PQEST</scope><scope>PQQKQ</scope><scope>PQUKI</scope><scope>PRINS</scope><scope>7X8</scope></search><sort><creationdate>200610</creationdate><title>Endovascular Repair of Dissecting Thoracic Aortic Aneurysm in a Patient with Turner Syndrome</title><author>Petrov, Ivo ; Nedevska, Maria ; Chilingirova, Nezabravka ; Simeonov, Peyo ; Kratunkov, Pencho ; Stoinova, Vesela ; Nikolov, Dimitar ; Konteva, Mariana ; Tzarianski, Georgi ; Tschirkov, Alexander I.</author></sort><facets><frbrtype>5</frbrtype><frbrgroupid>cdi_FETCH-LOGICAL-c341t-3f6ab80f70f74b553319b4e5ae3885700034cc96cc456420be977559d00fde433</frbrgroupid><rsrctype>articles</rsrctype><prefilter>articles</prefilter><language>eng</language><creationdate>2006</creationdate><topic>Adult</topic><topic>Aneurysm, Dissecting - diagnostic imaging</topic><topic>Aneurysm, Dissecting - etiology</topic><topic>Aneurysm, Dissecting - surgery</topic><topic>Aneurysms</topic><topic>Aortic Aneurysm, Thoracic - diagnostic imaging</topic><topic>Aortic Aneurysm, Thoracic - etiology</topic><topic>Aortic Aneurysm, Thoracic - surgery</topic><topic>Blood Vessel Prosthesis Implantation</topic><topic>Case studies</topic><topic>Female</topic><topic>Genetic disorders</topic><topic>Humans</topic><topic>Hypothyroidism</topic><topic>Medical treatment</topic><topic>Patients</topic><topic>Risk factors</topic><topic>Stents</topic><topic>Subclavian Artery - surgery</topic><topic>Tomography, X-Ray Computed</topic><topic>Turner Syndrome - complications</topic><topic>Turner Syndrome - diagnostic imaging</topic><topic>Vascular Patency</topic><topic>Vascular surgery</topic><topic>Veins & arteries</topic><toplevel>peer_reviewed</toplevel><toplevel>online_resources</toplevel><creatorcontrib>Petrov, Ivo</creatorcontrib><creatorcontrib>Nedevska, Maria</creatorcontrib><creatorcontrib>Chilingirova, Nezabravka</creatorcontrib><creatorcontrib>Simeonov, Peyo</creatorcontrib><creatorcontrib>Kratunkov, Pencho</creatorcontrib><creatorcontrib>Stoinova, Vesela</creatorcontrib><creatorcontrib>Nikolov, Dimitar</creatorcontrib><creatorcontrib>Konteva, Mariana</creatorcontrib><creatorcontrib>Tzarianski, Georgi</creatorcontrib><creatorcontrib>Tschirkov, Alexander I.</creatorcontrib><collection>Medline</collection><collection>MEDLINE</collection><collection>MEDLINE (Ovid)</collection><collection>MEDLINE</collection><collection>MEDLINE</collection><collection>PubMed</collection><collection>CrossRef</collection><collection>ProQuest Central (Corporate)</collection><collection>Nursing & Allied Health Database</collection><collection>ProQuest Health and Medical</collection><collection>ProQuest Central (purchase pre-March 2016)</collection><collection>Medical Database (Alumni Edition)</collection><collection>Hospital Premium Collection</collection><collection>Hospital Premium Collection (Alumni Edition)</collection><collection>ProQuest Central (Alumni) (purchase pre-March 2016)</collection><collection>ProQuest Central (Alumni)</collection><collection>ProQuest Central</collection><collection>AUTh Library subscriptions: ProQuest Central</collection><collection>ProQuest One Community College</collection><collection>Health Research Premium Collection</collection><collection>Health Research Premium Collection (Alumni)</collection><collection>ProQuest Health & Medical Complete (Alumni)</collection><collection>Nursing & Allied Health Database (Alumni Edition)</collection><collection>Health & Medical Collection (Alumni Edition)</collection><collection>Medical Database</collection><collection>Nursing & Allied Health Premium</collection><collection>ProQuest One Academic Eastern Edition (DO NOT USE)</collection><collection>ProQuest One Academic</collection><collection>ProQuest One Academic UKI Edition</collection><collection>ProQuest Central China</collection><collection>MEDLINE - Academic</collection><jtitle>Journal of endovascular therapy</jtitle></facets><delivery><delcategory>Remote Search Resource</delcategory><fulltext>fulltext</fulltext></delivery><addata><au>Petrov, Ivo</au><au>Nedevska, Maria</au><au>Chilingirova, Nezabravka</au><au>Simeonov, Peyo</au><au>Kratunkov, Pencho</au><au>Stoinova, Vesela</au><au>Nikolov, Dimitar</au><au>Konteva, Mariana</au><au>Tzarianski, Georgi</au><au>Tschirkov, Alexander I.</au><format>journal</format><genre>article</genre><ristype>JOUR</ristype><atitle>Endovascular Repair of Dissecting Thoracic Aortic Aneurysm in a Patient with Turner Syndrome</atitle><jtitle>Journal of endovascular therapy</jtitle><addtitle>J Endovasc Ther</addtitle><date>2006-10</date><risdate>2006</risdate><volume>13</volume><issue>5</issue><spage>693</spage><epage>696</epage><pages>693-696</pages><issn>1526-6028</issn><eissn>1545-1550</eissn><abstract>Purpose:
To report a rare case of dissecting thoracic aortic aneurysm in a young patient with Turner syndrome owing to complete or partial monosomy of the X chromosome.
Case Report:
A 22-year-old patient with Turner syndrome presented with a 2-month history of voice loss and dysphagia. Multislice computed tomography (MSCT) disclosed a large (53times75-mm) aneurysm with focal dissection affecting the distal part of the aortic arch and the proximal descending aorta, partially involving the left subclavian artery. A TAG endoprosthesis was implanted without complications. MSCT scans at 3 and 6 months after the procedure showed good position and patency of the stent-graft, with total exclusion and shrinkage of the aneurysm. After 1 year of follow-up, she is doing well, without voice disturbances or dysphagia.
Conclusion:
Although cardiovascular malformations are common in patients with Turner syndrome, dissecting thoracic aortic aneurysm is unusual. Stent-graft repair would appear to be feasible in this situation, but long-term implantation in young patients has not been explored.</abstract><cop>Los Angeles, CA</cop><pub>SAGE Publications</pub><pmid>17042655</pmid><doi>10.1583/05-1663.1</doi><tpages>4</tpages></addata></record> |
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| identifier | ISSN: 1526-6028 |
| ispartof | Journal of endovascular therapy, 2006-10, Vol.13 (5), p.693-696 |
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| language | eng |
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| source | Sage Journals Online |
| subjects | Adult Aneurysm, Dissecting - diagnostic imaging Aneurysm, Dissecting - etiology Aneurysm, Dissecting - surgery Aneurysms Aortic Aneurysm, Thoracic - diagnostic imaging Aortic Aneurysm, Thoracic - etiology Aortic Aneurysm, Thoracic - surgery Blood Vessel Prosthesis Implantation Case studies Female Genetic disorders Humans Hypothyroidism Medical treatment Patients Risk factors Stents Subclavian Artery - surgery Tomography, X-Ray Computed Turner Syndrome - complications Turner Syndrome - diagnostic imaging Vascular Patency Vascular surgery Veins & arteries |
| title | Endovascular Repair of Dissecting Thoracic Aortic Aneurysm in a Patient with Turner Syndrome |
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