Hirschsprung's disease in an infant with colonic atresia and normal fixation of the distal colon

Abstract The coexistence of colonic atresia and Hirschsprung's disease presents a diagnostic and therapeutic challenge. Colonic atresia is quickly recognized, and the majority of patients are diverted shortly after birth. The diagnosis of coincident Hirschsprung's disease usually is made a...

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Bibliographic Details
Published in:Journal of pediatric surgery 2007-02, Vol.42 (2), p.e5-e8
Main Authors: Draus, John M, Maxfield, Charles M, Bond, Sheldon J
Format: Article
Language:English
Subjects:
Abdomen, Acute - etiology
Abdomen, Acute - surgery
Anastomosis, Surgical
Biopsy, Needle
Colon - abnormalities
Digestive System Surgical Procedures - methods
Follow-Up Studies
Hirschsprung Disease - complications
Hirschsprung Disease - diagnosis
Hirschsprung Disease - surgery
Humans
Ileostomy - methods
Infant, Newborn
Intestinal Atresia - complications
Intestinal Atresia - diagnosis
Intestinal Atresia - surgery
Male
Pediatrics
Risk Assessment
Surgery
Treatment Outcome
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Summary:Abstract The coexistence of colonic atresia and Hirschsprung's disease presents a diagnostic and therapeutic challenge. Colonic atresia is quickly recognized, and the majority of patients are diverted shortly after birth. The diagnosis of coincident Hirschsprung's disease usually is made after anastomotic failure after restoration of intestinal continuity. A recent compilation of these patients has suggested that Hirschsprung's disease may be predicted on the basis of nonfixation of the colon distal to the atresia. However, we recently cared for an infant with transverse colonic atresia and total colonic aganglionosis associated with normal orientation and fixation of the distal colon.
ISSN:0022-3468
1531-5037
DOI:10.1016/j.jpedsurg.2006.10.021