Tracheal anomalies complicating ventilation of an infant with Apert syndrome

Abstract Apert syndrome is a rare autosomal dominant disorder characterized by severe syndactyly of the feet and hands, craniofacial abnormalities, and craniosynostosis. A 7-month-old male infant with Apert syndrome who underwent direct bronchoscopy and tracheotomy during general anesthesia is prese...

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Bibliographic Details
Published in:Journal of clinical anesthesia 2007-11, Vol.19 (7), p.551-554
Main Authors: Hutson, Larry R., MD, Young, Elizabeth, MD, Guarisco, Lindhe, MD
Format: Article
Language:English
Subjects:
Acrocephalosyndactylia - physiopathology
Airway management
Anesthesia
Anesthesia & Perioperative Care
Anesthesia, General
Anesthesia. Intensive care medicine. Transfusions. Cell therapy and gene therapy
Apert syndrome
Autosomal disorders
Babies
Biological and medical sciences
Bronchoscopy
Cardiac arrhythmia
Cartilage
Esophagus
General anesthesia
Humans
Hypoxia
Infant
Intubation
Laryngoscopy
Lungs
Male
Medical sciences
Ostomy
Pain Medicine
Patients
Pediatric anesthesia
Respiration, Artificial
Trachea - abnormalities
Tracheotomy
Ventilators
Vocal Cords - abnormalities
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Summary:Abstract Apert syndrome is a rare autosomal dominant disorder characterized by severe syndactyly of the feet and hands, craniofacial abnormalities, and craniosynostosis. A 7-month-old male infant with Apert syndrome who underwent direct bronchoscopy and tracheotomy during general anesthesia is presented. Early rigid bronchoscopy is important in these patients when there are problems with the airway, as they have a relatively high incidence of airway anomalies.
ISSN:0952-8180
1873-4529
DOI:10.1016/j.jclinane.2007.02.015