Successful surgical treatment of a neonate with prenatal diagnosis of severe Ebstein's anomaly

We present a case of a patient with a severe form of Ebstein's anomaly diagnosed in a 36th week of gestation through prenatal echocardiographic evaluation. The emergency surgery consisted of closure of the tricuspid valve and creation of a residual atriventricular communication, enlargement of...

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Bibliographic Details
Published in:Pediatric cardiology 2005-12, Vol.26 (6), p.869-871
Main Authors: Malec, E, Dangel, J, Mroczek, T, Procelewska, M, Januszewska, K, Ko Cz, J
Format: Article
Language:English
Subjects:
Adult
Arteriovenous Shunt, Surgical
Care and treatment
Diagnosis
Ebstein Anomaly - diagnostic imaging
Ebstein Anomaly - surgery
Ebstein's anomaly
Echocardiography
Female
Heart Ventricles - diagnostic imaging
Heart Ventricles - surgery
Humans
Infant, Newborn
Male
Pregnancy
Ultrasonography, Prenatal
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Summary:We present a case of a patient with a severe form of Ebstein's anomaly diagnosed in a 36th week of gestation through prenatal echocardiographic evaluation. The emergency surgery consisted of closure of the tricuspid valve and creation of a residual atriventricular communication, enlargement of interatrial communication, closure of the pulmonary artery, and construction of an aortopulmonary shunt. Subsequently, the patient underwent the hemiFontan and Fontan operation. We conclude that prenatal echocardiographic diagnosis is crucial for the survival of children with a severe form of Ebstein's anomaly, which is a neonatal emergency and requires prompt decision mating to initiate surgical management.
ISSN:0172-0643
1432-1971
DOI:10.1007/s00246-005-0987-3