The spine in diastrophic dysplasia : The surgical arthrodesis of thoracic and lumbar deformities in 21 patients

• Published in: Spine (Philadelphia, Pa. 1976) Pa. 1976), 1999-11, Vol.24 (22), p.2325-2331
• Main Authors: MATSUYAMA, Y, WINTER, R. B, LONSTEIN, J. E
• Format: Article
• Language: English
• Subjects: Adolescent; Adult; Biological and medical sciences; Bone Diseases, Developmental - diagnostic imaging; Bone Diseases, Developmental - surgery; Child; Diseases of the osteoarticular system; Female; Follow-Up Studies; Humans; Kyphosis - diagnostic imaging; Kyphosis - surgery; Lumbar Vertebrae - abnormalities; Lumbar Vertebrae - surgery; Malformations and congenital and or hereditary diseases involving bones. Joint deformations; Medical sciences; Radiography; Scoliosis - diagnostic imaging; Scoliosis - surgery; Spinal Fusion; Thoracic Vertebrae - abnormalities; Thoracic Vertebrae - surgery; Time Factors; Treatment Outcome
• ISSN: 0362-2436; 1528-1159
• DOI: 10.1097/00007632-199911150-00007

Retrospective chart and radiographic film review. To discern the deformity problems in diastrophic dysplasia and to report our results in surgical treatment. Due to the rarity of the problem, the literature is very scanty as to the indications for surgery or the best technique. Analysis of radiographic film for scoliosis, kyphosis, lordosis, and decompensation before surgery, after surgery, and at follow-up. Analysis of charts for complications and problems. The most common deformity pattern was a double thoracic kyphosis (79 degrees/97 degrees) with a true kyphosis at the junction of the two scolioses (101 degrees). Combined anterior-posterior arthrodesis gave the best results. Very severe deformity can occur in children with diastrophic dysplasia, even at a young age. Prompt anterior-posterior arthrodesis can prevent catastrophic deformity.