Progressive bone resorption after pathological fracture of the femoral neck in Hunter's syndrome

We report a case of Hunter's syndrome associated with a transverse fracture of the left femoral neck after minor trauma, followed by progressive resorption of the femoral head at 12 years of age and a stress fracture of the right femoral neck at 16 years of age. MRI performed at 15 years of age...

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Bibliographic Details
Published in:Pediatric radiology 1999-12, Vol.29 (12), p.914-916
Main Authors: ICHIKAWA, T, NISHIMURA, G, TSUKUNE, Y, DEZAWA, A, MIKI, H
Format: Article
Language:English
Subjects:
Biological and medical sciences
Bone Resorption - diagnosis
Bone Resorption - diagnostic imaging
Bone Resorption - etiology
Carbohydrates (enzymatic deficiencies). Glycogenosis
Child
Disease Progression
Errors of metabolism
Femoral Neck Fractures - complications
Femur Head - diagnostic imaging
Femur Head - pathology
Fractures, Spontaneous - complications
Humans
Magnetic Resonance Imaging
Male
Medical sciences
Metabolic diseases
Mucopolysaccharidosis II - complications
Radiography
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Summary:We report a case of Hunter's syndrome associated with a transverse fracture of the left femoral neck after minor trauma, followed by progressive resorption of the femoral head at 12 years of age and a stress fracture of the right femoral neck at 16 years of age. MRI performed at 15 years of age revealed intra-articular low intensity on T1-weighted and T2-weighted images of both hip joints. The MR finding may represent fibrous synovial thickening, which caused pressure erosion of the femoral neck, resultant pathological and/or stress fractures, and subsequent osteonecrosis with rapid absorption of the femoral head.
ISSN:0301-0449
1432-1998
DOI:10.1007/s002470050725