Rare association of hypertrophic cardiomyopathy and complete atrioventricular block with prompt disappearance of outflow gradient after DDD pacing

Although arrhythmias are common in hypertrophic cardiomyopathy (HCM), complete atrioventricular (AV) block is very unusual. A 27-year-old female presented with a recent history of syncope and exercise intolerance. ECG demonstrated complete AV block. Two-dimensional Doppler echocardiography revealed...

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Bibliographic Details
Published in:Europace (London, England) England), 1999-10, Vol.1 (4), p.280-282
Main Authors: Yesil, M, Bayata, S, Susam, I, Dinçkal, H, Postaci, N
Format: Article
Language:English
Subjects:
Adult
Cardiac Pacing, Artificial
Cardiomyopathy, Hypertrophic - complications
Electrocardiography
Female
Heart Block - diagnosis
Heart Block - etiology
Heart Block - physiopathology
Humans
Recurrence
Syncope - etiology
Ventricular Dysfunction, Left - etiology
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Summary:Although arrhythmias are common in hypertrophic cardiomyopathy (HCM), complete atrioventricular (AV) block is very unusual. A 27-year-old female presented with a recent history of syncope and exercise intolerance. ECG demonstrated complete AV block. Two-dimensional Doppler echocardiography revealed HCM with a 60 mmHg left ventricular outflow tract (LVOT) gradient. A temporary transvenous ventricular pacemaker was inserted urgently, and subsequently replaced by a permanent DDD pacemaker. All symptoms were eliminated. This symptomatic improvement was associated with complete disappearance of LVOT gradient at the time of implantation. No gradient was observed during early follow-up and at 6 months after DDD pacemaker implantation.
ISSN:1099-5129
DOI:10.1053/eupc.1999.0051