Familial pulmonary hypoplasia : plain film appearances with histopathological correlation

Familial pulmonary hypoplasia is a rare cause of bilateral pulmonary hypoplasia. We describe the plain film appearances and correlate these with the histopathological findings in an infant who survived 5 weeks. In this case, improved technology prolonged survival, allowing the radiological appearanc...

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Bibliographic Details
Published in:Pediatric radiology 1999-06, Vol.29 (6), p.455-458
Main Authors: GREEN, R. A. R, SHAW, D. G, HAWORTH, S. G
Format: Article
Language:English
Subjects:
Adult
Biological and medical sciences
Fatal Outcome
Female
Humans
Infant, Newborn
Lung - abnormalities
Lung - diagnostic imaging
Lung Diseases - diagnostic imaging
Lung Diseases - genetics
Lung Diseases - pathology
Medical sciences
Pneumology
Radiography, Thoracic
Respiratory system : syndromes and miscellaneous diseases
Citations: Items that cite this one
Online Access:Get full text
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Description
Summary:Familial pulmonary hypoplasia is a rare cause of bilateral pulmonary hypoplasia. We describe the plain film appearances and correlate these with the histopathological findings in an infant who survived 5 weeks. In this case, improved technology prolonged survival, allowing the radiological appearance of the primitive lung architecture to become more clearly defined.
ISSN:0301-0449
1432-1998
DOI:10.1007/s002470050616