Protracted superficial Wegener granulomatosis in a child

Wegener granulomatosis is a rare, chronic, multisystemic vasculitis affecting mainly the upper and lower respiratory tracts together with glomerulonephritis, but the disease may involve any other organ. Protracted superficial form is a rare variant of the disease. We report a case of protracted supe...

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Bibliographic Details
Published in:Dermatology online journal 2007-10, Vol.13 (4), p.14-14
Main Authors: Ben Ghorbel, Imed, Dhrif, Asma Sioud, Miled, Mohamed, Houman, Mohamed Habib
Format: Article
Language:English
Subjects:
Adolescent
Fingers
Glucocorticoids - therapeutic use
Granulomatosis with Polyangiitis - complications
Granulomatosis with Polyangiitis - drug therapy
Humans
Male
Nasal Mucosa
Prednisone - therapeutic use
Skin Ulcer - etiology
Toes
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Summary:Wegener granulomatosis is a rare, chronic, multisystemic vasculitis affecting mainly the upper and lower respiratory tracts together with glomerulonephritis, but the disease may involve any other organ. Protracted superficial form is a rare variant of the disease. We report a case of protracted superficial Wegener granulomatosis in a 16-year-old boy in whom the disease started with recurrent digital ulcers at age 7 years. Later, he developed nodules and papules associated with upper airway involvement and ocular keratitis without lung or renal involvement. C-ANCA was positive. The patient was treated with oral prednisone. Similar cutaneous and mucosal lesions developed during two relapses of the disease without renal or respiratory involvement.
ISSN:1087-2108
1087-2108
DOI:10.5070/D30JX1H2P5