Clear cell sarcoma of soft tissues

Clear cell sarcoma (CCS) is a rare but highly malignant tumor of soft tissues often appearing as a small tender mass in the deep tissues of the distal extremities. We have studied 17 patients with such lesions treated since 1986 and have a high incidence of local recurrence and metastasis with a sur...

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Bibliographic Details
Published in:Journal of surgical oncology 2007-05, Vol.95 (6), p.519-522
Main Authors: Malchau, Sara Sofia, Hayden, James, Hornicek, Francis, Mankin, Henry J.
Format: Article
Language:English
Subjects:
Adolescent
Adult
Aged
Child
clear cell sarcoma
Combined Modality Therapy
Extremities
Female
Humans
Magnetic Resonance Imaging
Male
Middle Aged
outcome
Proportional Hazards Models
Sarcoma, Clear Cell - mortality
Sarcoma, Clear Cell - pathology
Sarcoma, Clear Cell - radiotherapy
Sarcoma, Clear Cell - surgery
Soft Tissue Neoplasms - mortality
Soft Tissue Neoplasms - pathology
Soft Tissue Neoplasms - radiotherapy
Soft Tissue Neoplasms - surgery
Survival Rate
treatment
Treatment Outcome
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Description
Summary:Clear cell sarcoma (CCS) is a rare but highly malignant tumor of soft tissues often appearing as a small tender mass in the deep tissues of the distal extremities. We have studied 17 patients with such lesions treated since 1986 and have a high incidence of local recurrence and metastasis with a survival rate of only 47% despite surgery and for many of the patients, adjuvant therapy. The purpose of this article is to warn the readers of the dangers related to treating this seemingly benign lesion and urge them to perform wide surgery and utilize adjuvant therapy. J. Surg. Oncol. 2007; 95: 519–522. © 2006 Wiley‐Liss, Inc.
ISSN:0022-4790
1096-9098
DOI:10.1002/jso.20730