Biliary atresia associated with multiple unrelated anomalies: what about it?

The prognosis of extrahepatic biliary atresia (EHBA) and multiple apparently not linked anomalies has never been disclosed. We reported a rare case affected by biliary, anorectal and esophageal atresia, and collected the uncommon associations of EHBA with multiple unrelated congenital defects to mak...

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Bibliographic Details
Published in:Pediatric surgery international 2007-03, Vol.23 (3), p.277-280
Main Authors: Casaccia, G, Catalano, O A, Marcellini, M, Bagolan, P
Format: Article
Language:English
Subjects:
Abnormalities, Multiple
Biliary Atresia
Digestive System Abnormalities
Humans
Infant, Newborn
Male
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Summary:The prognosis of extrahepatic biliary atresia (EHBA) and multiple apparently not linked anomalies has never been disclosed. We reported a rare case affected by biliary, anorectal and esophageal atresia, and collected the uncommon associations of EHBA with multiple unrelated congenital defects to make known the prognosis. An elevated rate of hepatic failure despite surgery and an early poor outcome were found in the above-mentioned associations. A liver transplantation at the first months of life could be considered to improve outcome.
ISSN:0179-0358
1437-9813
DOI:10.1007/s00383-006-1780-y