En bloc heterotopic auxiliary liver and bilateral renal transplant in a patient with homozygous protein C deficiency

An 8-year-old girl with homozygous protein C deficiency who had undergone maintenance dialysis since birth because of renal veins with thrombosis was treated with an en bloc heterotopic auxiliary liver and bilateral renal transplantation. The reconstitution of protein C activity by auxiliary liver t...

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Bibliographic Details
Published in:The Journal of pediatrics 2001-01, Vol.138 (1), p.120-122
Main Authors: Angelis, Michael, Pegelow, Charles H., Khan, Farrukh A., Verzaro, Roberto, Tzakis, Andreas G.
Format: Article
Language:English
Subjects:
Biological and medical sciences
Child
Choledochostomy
Female
Homozygote
Humans
Kidney Failure, Chronic - etiology
Kidney Failure, Chronic - surgery
Kidney Transplantation - methods
Liver Transplantation - methods
Liver, biliary tract, pancreas, portal circulation, spleen
Medical sciences
Phenotype
Protein C Deficiency - complications
Protein C Deficiency - genetics
Protein C Deficiency - surgery
Renal Dialysis
Renal Veins
Surgery (general aspects). Transplantations, organ and tissue grafts. Graft diseases
Surgery of the digestive system
Transplantation, Heterotopic - methods
Venous Thrombosis - etiology
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Summary:An 8-year-old girl with homozygous protein C deficiency who had undergone maintenance dialysis since birth because of renal veins with thrombosis was treated with an en bloc heterotopic auxiliary liver and bilateral renal transplantation. The reconstitution of protein C activity by auxiliary liver transplantation facilitated successful renal transplantation. (J Pediatr 2001;138:120-2)
ISSN:0022-3476
1097-6833
DOI:10.1067/mpd.2001.109199