Oral lesions in recessive dystrophic epidermolysis bullosa

Objective:  To study the prevalence of oral lesions in 35 patients diagnosed with generalized recessive dystrophic epidermolysis bullosa (RDEBg), with a quantification of their microstomia in comparison with a control group. Material and methods:  The presence of oral mucosal lesions and interincisa...

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Bibliographic Details
Published in:Oral diseases 2003-09, Vol.9 (5), p.264-268
Main Authors: Serrano-Martínez, MC, Bagán, JV, Silvestre, FJ, Viguer, MT
Format: Article
Language:English
Subjects:
Adolescent
Adult
Atrophy
Biological and medical sciences
Blister - etiology
Bullous diseases of the skin
Child
Child, Preschool
Dentistry
Dermatology
Epidermolysis Bullosa Dystrophica - complications
Female
Fibrosis
Humans
Male
Medical sciences
Microstomia - etiology
Mouth Diseases - etiology
Non tumoral diseases
oral blisters
Otorhinolaryngology. Stomatology
Palate - pathology
recessive dystrophic epidermolysis bullosa
Tongue - abnormalities
Tongue Diseases - etiology
Upper respiratory tract, upper alimentary tract, paranasal sinuses, salivary glands: diseases, semeiology
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Summary:Objective:  To study the prevalence of oral lesions in 35 patients diagnosed with generalized recessive dystrophic epidermolysis bullosa (RDEBg), with a quantification of their microstomia in comparison with a control group. Material and methods:  The presence of oral mucosal lesions and interincisal maximum oral aperture (MOA) was determined, classifying microstomia according to the method of Naylor, Douglass and Mix (1984). Results:  Blister lesions were identified in 92% of the patients at the time of exploration – the tongue being the most affected location. Microstomia and palatal atrophy were the most prevalent sequelae (100%), while ankyloglossia, vestibular obliteration and lingual depapillation were recorded in over 90%. In 80% of the patients interincisal MOA was
ISSN:1354-523X
1601-0825
DOI:10.1034/j.1601-0825.2003.03971.x