Ventricular tachycardia associated with isolated right ventricular dysfunction as indicator of arrhythmogenic dysplasia of the right ventricle

We report the case of a 21 year-old patient with arrhythmogenic right ventricular dysplasia manifested by episodes of QRS tachycardia greater than 0.12 sec and isolated dysfunction of the right ventricle. The patient treated with amiodarone however, the tachycardia episodes persisted. The surface el...

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Bibliographic Details
Published in:Archivos de cardiología de México 2001-10, Vol.71 (4), p.324-329
Main Authors: Rojel Martínez, U, Colín Lizalde, L, Guevara-Valdivia, M E, Iturralde, P, Rodríguez, I
Format: Article
Language:Spanish
Subjects:
Adult
Arrhythmogenic Right Ventricular Dysplasia - complications
Arrhythmogenic Right Ventricular Dysplasia - diagnosis
Female
Humans
Tachycardia, Ventricular - complications
Ventricular Dysfunction, Right - complications
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Summary:We report the case of a 21 year-old patient with arrhythmogenic right ventricular dysplasia manifested by episodes of QRS tachycardia greater than 0.12 sec and isolated dysfunction of the right ventricle. The patient treated with amiodarone however, the tachycardia episodes persisted. The surface electrocardiogram showed left branch block with the axis down, which suggested a right ventricle origin, and was therefore considered an arrhythmogenic dysplasia. Echocardiography and cardioangiography showed alterations in the anatomy of the outflow tract of the right ventricle. A myocardial gammagraphy revealed no perfusion alterations. The endomyocardial biopsy showed perivascular fibrosis. An electrophysiology study was performed, stimulating the outflow tract of the right ventricle, which induced two types of ventricular tachycardias, one of them identical to that recorded clinical. The patient was treated with sotalol, and has been being free of ventricular tachycardia episodes for 18 months of follow-up. We consider that this entity should be studied in a systematic way in those patients with ventricular tachycardia originated in the outflow of the right ventricle and with primary cardiac illness.
ISSN:1405-9940