Rosai-Dorfman disease of the subglottis

A case of subglottic narrowing caused by an extranodal deposit of sinus histiocytosis in a 29-year-old man is reported. The characteristic features of Rosai-Dorfman disease, such as massive painless cervical lymphadenopathy, fever, raised erythrocyte sedimentation rate and raised white cell count, w...

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Bibliographic Details
Published in:Journal of laryngology and otology 2000-12, Vol.114 (12), p.970-973
Main Authors: Hazarika, Produl, Nayak, Deepak R., Balakrishnan, R., Kundaje, Harish G., Rao, P. Lakshmi
Format: Article
Language:English
Subjects:
(RF) Otorhinolaryngology
Adult
Anti-Inflammatory Agents - therapeutic use
Biological and medical sciences
Biopsy
Diagnosis, Differential
Hematologic and hematopoietic diseases
Histiocytosis Sinus
Histiocytosis, Sinus - diagnosis
Histiocytosis, Sinus - etiology
Histiocytosis, Sinus - therapy
Humans
Laryngeal Diseases - diagnosis
Laryngeal Diseases - etiology
Laryngeal Diseases - therapy
Larynx
Male
Medical sciences
Non tumoral diseases
Other diseases. Hematologic involvement in other diseases
Otorhinolaryngology. Stomatology
Prednisolone - therapeutic use
Tomography, X-Ray Computed
Tracheostomy
Upper respiratory tract, upper alimentary tract, paranasal sinuses, salivary glands: diseases, semeiology
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Summary:A case of subglottic narrowing caused by an extranodal deposit of sinus histiocytosis in a 29-year-old man is reported. The characteristic features of Rosai-Dorfman disease, such as massive painless cervical lymphadenopathy, fever, raised erythrocyte sedimentation rate and raised white cell count, were all found to be absent. However, typical histological features, such as diffuse lymphoplasmacytic infiltrate, Russel bodies, foamy histiocytes and histiocytes with emperipoiesis, confirmed the diagnosis. Rosai-Dorfman disease is an uncommon disorder and its presentation with progressive subglottic narrowing is extremely rare. Our experience in the management of this condition is reported and the review of literature is discussed.
ISSN:0022-2151
1748-5460
DOI:10.1258/0022215001904491