A spinal intradural enterogenous cyst with well-differentiated muscularis propria

We report a case of a newborn presenting with severe compression of the spinal cord due to a large, solitary mass extending from C4 to T2. Neurosurgical exploration revealed a large intradural, extramedullary cystic lesion, compressing the spinal cord. Slowly progressive respiratory failure due to s...

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Bibliographic Details
Published in:Acta neuropathologica 2002-11, Vol.104 (5), p.538-542
Main Authors: TEN DONKELAAR, H. J, WILLEMSEN, M. A. A. P, VAN DER HEIJDEN, I, BEEMS, T, WESSELING, P
Format: Article
Language:English
Subjects:
Biological and medical sciences
Cervical Vertebrae
Cysts - complications
Cysts - pathology
Female
Humans
Infant, Newborn
Medical sciences
Neurology
Spinal Cord Compression - etiology
Spinal Cord Diseases - pathology
Thoracic Vertebrae
Tumors of the nervous system. Phacomatoses
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Summary:We report a case of a newborn presenting with severe compression of the spinal cord due to a large, solitary mass extending from C4 to T2. Neurosurgical exploration revealed a large intradural, extramedullary cystic lesion, compressing the spinal cord. Slowly progressive respiratory failure due to severe myelopathy led to the death of the child 19 days postpartum. At autopsy, a well-differentiated enterogenous cyst was found, the cyst wall containing gastric and esophageal type mucosa, and a bona fide muscularis propria. The gastrointestinal tract was completely normal. The possible developmental history of intradural enterogenous cysts is discussed.
ISSN:0001-6322
1432-0533
DOI:10.1007/s00401-002-0599-4