Plastic bronchitis: an unusual bronchoscopic challenge associated with congenital heart disease repair

Plastic bronchitis is a rare disorder characterized by the formation of branching mucoid bronchial casts. Several pathophysiologic conditions are associated with development of these intrabronchial casts, including congenital heart defects. The management of plastic bronchitis presents an unusual an...

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Bibliographic Details
Published in:International journal of pediatric otorhinolaryngology 2003-05, Vol.67 (5), p.543-548
Main Authors: Ishman, Stacey, Book, David T., Conley, Stephen F., Kerschner, Joseph E.
Format: Article
Language:English
Subjects:
Biological and medical sciences
Bronchial casts
Bronchitis - complications
Bronchitis - etiology
Bronchitis - surgery
Bronchoscopy
Cardiology. Vascular system
Child, Preschool
Congenital heart diseases. Malformations of the aorta, pulmonary vessels and vena cava
Fontan Procedure
Heart
Heart Defects, Congenital - surgery
Humans
Laryngoscopy
Male
Medical sciences
Plastic bronchitis
Pneumology
Postoperative Complications - surgery
Recurrence
Respiratory Insufficiency - etiology
Respiratory system : syndromes and miscellaneous diseases
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Summary:Plastic bronchitis is a rare disorder characterized by the formation of branching mucoid bronchial casts. Several pathophysiologic conditions are associated with development of these intrabronchial casts, including congenital heart defects. The management of plastic bronchitis presents an unusual and interesting bronchoscopic challenge. We describe a patient who underwent a Fontan procedure for correction of a congenital heart defect and subsequently developed respiratory distress secondary to plastic bronchitis on two occasions. In both cases, endoscopic intervention was required to remove these casts. A review of the literature, including the proposed etiologies, diagnosis, and current medical and surgical management, is also undertaken.
ISSN:0165-5876
1872-8464
DOI:10.1016/S0165-5876(03)00004-1