case of Hughes-Stovin syndrome associated with hyperhomocysteinemia

We report a case of Hughes-Stovin syndrome (HSS) associated with hyperhomocysteinemia. A 24-year-old man who has no clinical features suggestive of Behcet's disease was admitted for hemoptysis and dyspnea. Radiological and laboratory evaluation revealed multifocal pulmonary artery aneurysms inv...

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Bibliographic Details
Published in:Clinical rheumatology 2010-07, Vol.29 (7), p.807-809
Main Authors: Kim, Hyun-Ok, Kim, Ho Cheol, Park, Yongwhi, Jeong, Yong-Geun, Kim, Jae Hee, Jeon, Dae-Hong, Jeon, Kyoung-Nyeo, Lee, Sang-Il
Format: Article
Language:English
Subjects:
aneurysm
Anti-Inflammatory Agents - therapeutic use
Anticoagulants - therapeutic use
Behcet's disease
Case Report
Dyspnea - complications
Dyspnea - drug therapy
Folic Acid - therapeutic use
Hematinics - therapeutic use
Hemoptysis - complications
Hemoptysis - drug therapy
Hughes-Stovin syndrome
Humans
Hyperhomocysteinemia
Hyperhomocysteinemia - complications
Hyperhomocysteinemia - drug therapy
Male
Medicine
Medicine & Public Health
Prednisolone - therapeutic use
Rheumatology
Syndrome
Treatment Outcome
Warfarin - therapeutic use
Young Adult
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Summary:We report a case of Hughes-Stovin syndrome (HSS) associated with hyperhomocysteinemia. A 24-year-old man who has no clinical features suggestive of Behcet's disease was admitted for hemoptysis and dyspnea. Radiological and laboratory evaluation revealed multifocal pulmonary artery aneurysms involving bilateral segmental pulmonary artery, thrombi in right atrium and ventricle, and hyperhomocysteinemia. Accordingly, HSS associated with hyperhomocysteinemia was diagnosed, and the clinical and radiological improvement was achieved after treatment with prednisolone, warfarin, and folic acid.
ISSN:0770-3198
1434-9949
DOI:10.1007/s10067-010-1393-7