Unilateral Ovarian Dermoid Cyst Accompanied by an Ipsilateral Paratubal Cyst in a Girl with Proteus Syndrome Discovered by Laparoscopic Surgery

Abstract Background Proteus syndrome is a rare hamartomatous disorder characterized by the overgrowth of multiple tissues in a mosaic pattern. Tumors of genitourinary tract in Proteus syndrome are uncommon. Case We here report a 5-year-old girl with Proteus syndrome who developed a cystic mass in th...

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Bibliographic Details
Published in:Journal of pediatric & adolescent gynecology 2010-06, Vol.23 (3), p.e107-e110
Main Authors: Hong, Jin Hwa, MD, Lee, Jae Kwan, MD, Song, Seung Hun, MD, Hwang, Jong Ha, MD, So, Kyung A., MD, Shin, Bong Kyung, MD, Lee, Nak Woo, MD, Lee, Kyu Wan, MD
Format: Article
Language:English
Subjects:
Child, Preschool
Dermoid cyst
Dermoid Cyst - complications
Dermoid Cyst - pathology
Dermoid Cyst - surgery
Female
Humans
Incidental Findings
Laparoscopic surgery
Laparoscopy
Obstetrics and Gynecology
Ovarian Cysts - complications
Ovarian Cysts - pathology
Ovarian Cysts - surgery
Paratubal cyst
Parovarian Cyst - complications
Parovarian Cyst - diagnosis
Parovarian Cyst - surgery
Pediatrics
Proteus syndrome
Proteus Syndrome - complications
Teratoma - complications
Teratoma - pathology
Teratoma - surgery
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Summary:Abstract Background Proteus syndrome is a rare hamartomatous disorder characterized by the overgrowth of multiple tissues in a mosaic pattern. Tumors of genitourinary tract in Proteus syndrome are uncommon. Case We here report a 5-year-old girl with Proteus syndrome who developed a cystic mass in the pelvic cavity. The cyst was discovered by ultrasonographic examination and finally proved to be a unilateral ovarian dermoid cyst accompanied by an ipsilateral paratubal cyst by laparoscopic surgery. Summary and Conclusion Proteus syndrome accompanied by an ovarian cyst is rare in girls. The possibilities of underlying ovarian cyst required for surgical intervention should be considered in Proteus syndrome.
ISSN:1083-3188
1873-4332
DOI:10.1016/j.jpag.2009.08.010