Rhegmatogenous retinal detachment in Wyburn-Mason syndrome: case report

Wyburn-Mason is a rare vascular disorder, comprised of arteriovenous malformations (AVMs) of the midbrain and retina. It can cause visual symptoms depending on its localization and extension. Vitreous and intraretinal hemorrhage and neovascular glaucoma have been previously described. A case of rheg...

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Bibliographic Details
Published in:Arquivos brasileiros de oftalmologia 2010-01, Vol.73 (1), p.88-91
Main Authors: Medina, Flávio MacCord, Maia, Jr, Otacílio de Oliveira, Takahashi, Walter Yukihiko
Format: Article
Language:English
Subjects:
Adult
Female
Humans
Intracranial Arteriovenous Malformations - complications
Retinal Artery - abnormalities
Retinal Detachment - diagnosis
Retinal Detachment - etiology
Retinal Detachment - surgery
Retinal Vein - abnormalities
Silicone Oils - therapeutic use
Syndrome
Vitrectomy
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Summary:Wyburn-Mason is a rare vascular disorder, comprised of arteriovenous malformations (AVMs) of the midbrain and retina. It can cause visual symptoms depending on its localization and extension. Vitreous and intraretinal hemorrhage and neovascular glaucoma have been previously described. A case of rhegmatogenous retinal detachment in a patient with Wyburn-Mason syndrome is described. A 27 year-old woman previously diagnosed with Wyburn-Mason syndrome, sought attendance with sudden low vision in right eye 3 months before. She presented moderate vitreous hemorrhage and retinal detachment with a superior tear. She underwent a successful posterior vitrectomy with implantation of silicone oil, with reattachment of the retina. Rhegmatogenous retinal detachment in a patient with Wyburn-Mason syndrome has been not previously described in the literature. Vitrectomy in this case present challenges related to intraoperatory bleeding risk, to a posterior pole tear among AVMs and the difficulty of obtaining free retina for photocoagulation.
ISSN:0004-2749
1678-2925
DOI:10.1590/S0004-27492010000100017