SAPHO syndrome with ankylosis of the temporomandibular joint

Abstract SAPHO syndrome is a rare combination of different symptoms with unknown aetiology. A complete ankylosis of the temporomandibular joint (TMJ) in a patient with SAPHO syndrome has not been described previously. The goal of this case report is to present the disease, give an overview about the...

Full description

Saved in:
Bibliographic Details
Published in:International journal of oral and maxillofacial surgery 2009-12, Vol.38 (12), p.1335-1341
Main Authors: Müller-Richter, U.D.A, Roldán, J.C, Mörtl, M, Behr, M, Reichert, T.E, Driemel, O
Format: Article
Language:English
Subjects:
Acquired Hyperostosis Syndrome - complications
Adult
ankylosis
Ankylosis - etiology
Arthroplasty, Replacement
Bacterial arthritis and osteitis
Bacterial diseases
Biological and medical sciences
Dentistry
Female
Follow-Up Studies
Human bacterial diseases
Humans
Image Processing, Computer-Assisted
Infectious diseases
mandible
Mandibular Condyle - pathology
Mandibular Diseases - complications
Medical sciences
osteomyelitis
Otorhinolaryngology. Stomatology
Reconstructive Surgical Procedures - methods
SAPHO syndrome
Surgery
temporomandibular joint
Temporomandibular Joint Disorders - etiology
Tomography, X-Ray Computed
Citations: Items that this one cites
Items that cite this one
Online Access:Get full text
Tags: Add Tag
No Tags, Be the first to tag this record!
Description
Summary:Abstract SAPHO syndrome is a rare combination of different symptoms with unknown aetiology. A complete ankylosis of the temporomandibular joint (TMJ) in a patient with SAPHO syndrome has not been described previously. The goal of this case report is to present the disease, give an overview about the frequency of mandibular involvement and describe different therapeutic strategies. The complication of an ankylosis of the TMJ is noted and the literature is reviewed. The authors report a 42-year-old patient with SAPHO syndrome and recurrent swelling of the right mandible and the soft tissue. The persisting involvement of the mandible resulted in a complete osseous ankylosis of the right TMJ and required resection with alloplastic replacement of the right condyle. SAPHO syndrome should be suspected in some cases of ‘therapy resistant osteomyelitis’ of the mandible. Smaller joints, such as the TMJ may also be affected. Treatment of SAPHO syndrome should include antibiotics and NSAIDs; corticosteroids may be helpful. Surgery is the ultimate treatment.
ISSN:0901-5027
1399-0020
DOI:10.1016/j.ijom.2009.03.724