Tracheal chondrosarcoma--a rare complication in Maffucci syndrome

Maffucci syndrome is a rare congenital non-hereditary disease characterised by subcutaneous haemangiomata and multiple enchondromata. We present a case of an intermediate grade myxoid chondrosarcoma of the tracheal cartilage in a 34-year-old man with a history of Maffucci syndrome. Chondrosarcoma of...

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Bibliographic Details
Published in:British journal of radiology 2009-09, Vol.82 (981), p.e178-e181
Main Authors: Wagnetz, U, Patsios, D, Darling, G, Las Heras, F, Hwang, D
Format: Article
Language:English
Subjects:
Adult
Bone Neoplasms - diagnostic imaging
Bone Neoplasms - etiology
Bone Neoplasms - pathology
Bronchoscopy
Chondrosarcoma - diagnostic imaging
Chondrosarcoma - etiology
Chondrosarcoma - pathology
Contrast Media
Enchondromatosis - complications
Humans
Male
Tomography, Spiral Computed - methods
Tracheal Neoplasms - diagnostic imaging
Tracheal Neoplasms - etiology
Tracheal Neoplasms - pathology
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Summary:Maffucci syndrome is a rare congenital non-hereditary disease characterised by subcutaneous haemangiomata and multiple enchondromata. We present a case of an intermediate grade myxoid chondrosarcoma of the tracheal cartilage in a 34-year-old man with a history of Maffucci syndrome. Chondrosarcoma of the trachea are extremely rare tumours. A review of the radiological literature reveals approximately 15 previously published cases. No case was found with a history of Maffucci syndrome.
ISSN:0007-1285
1748-880X
DOI:10.1259/bjr/17386896