Pyloric stenosis in an iniencephalic infant with a congenital intra-thoracic stomach

We report the first case of hypertrophic pyloric stenosis in an intrathoracic stomach in a neonate with congenital ultra-short oesophagus and iniencephaly clausus. Antenatal ultrasound detected right-sided thoracic cystic lesions and postnatal investigations revealed an intra-thoracic stomach and sp...

Full description

Saved in:
Bibliographic Details
Published in:Pediatric surgery international 2009-10, Vol.25 (10), p.907-909
Main Authors: Winckworth, Lucinda C., Rees, Clare M., Fan, Tiffany, Haddad, Munther, Clarke, Simon A.
Format: Article
Language:English
Subjects:
Case Report
Female
Humans
Infant, Newborn
Medicine
Medicine & Public Health
Neural Tube Defects - complications
Pediatric Surgery
Pediatrics
Pyloric Stenosis, Hypertrophic - complications
Pyloric Stenosis, Hypertrophic - surgery
Stomach Diseases - complications
Stomach Diseases - congenital
Stomach Diseases - surgery
Surgery
Citations: Items that this one cites
Items that cite this one
Online Access:Get full text
Tags: Add Tag
No Tags, Be the first to tag this record!
Description
Summary:We report the first case of hypertrophic pyloric stenosis in an intrathoracic stomach in a neonate with congenital ultra-short oesophagus and iniencephaly clausus. Antenatal ultrasound detected right-sided thoracic cystic lesions and postnatal investigations revealed an intra-thoracic stomach and spleen with an ultra-short oesophagus and intact diaphragm. Subsequently, she developed pyloric stenosis. Such neonates require urgent referral to surgical centres for what is a challenging diagnosis and complicated management.
ISSN:0179-0358
1437-9813
DOI:10.1007/s00383-009-2479-7