Early myoclonic encephalopathy

Early myoclonic encephalopathy (EME) is a rare malignant epileptic syndrome. The erratic myoclonus with or without focal motor seizures, onset before 3 months of age, and persistent suppression-burst pattern in electroencephalograph (EEG) are accepted as the diagnostic criteria for EME. We report an...

Full description

Saved in:
Bibliographic Details
Published in:Indian pediatrics 2009-09, Vol.46 (9), p.804-806
Main Authors: Kamate, Mahesh, Mahantshetti, Niranjana, Chetal, Vivek
Format: Article
Language:English
Subjects:
Anticonvulsants - therapeutic use
Electroencephalography - methods
Epilepsies, Myoclonic - diagnosis
Epilepsies, Myoclonic - drug therapy
Epilepsies, Myoclonic - etiology
Humans
Hyperglycinemia, Nonketotic - complications
Hyperglycinemia, Nonketotic - diagnosis
Infant
Male
Online Access:Get full text
Tags: Add Tag
No Tags, Be the first to tag this record!
Description
Summary:Early myoclonic encephalopathy (EME) is a rare malignant epileptic syndrome. The erratic myoclonus with or without focal motor seizures, onset before 3 months of age, and persistent suppression-burst pattern in electroencephalograph (EEG) are accepted as the diagnostic criteria for EME. We report an 11 month old infant with EME which was secondary to non-ketotic hyperglycinemia.
ISSN:0974-7559