Anesthetic management for foramen magnum decompression in a patient with Morquio syndrome: a case report

Morquio syndrome is a hereditary mucopolysaccharide disorder presenting with an abnormality of the craniocervical junction from childhood. We describe an adult patient who presented with Morquio syndrome who had subglottic narrowing of the airway, restrictive pulmonary disease, and mild mitral regur...

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Bibliographic Details
Published in:Journal of anesthesia 2010-08, Vol.24 (4), p.594-597
Main Authors: Geetha, Lakshminarsimhaiah, Radhakrishnan, Muthuchellappan, Raghavendra, Biligiri Sridhar, Rao, G. S. Umamaheswara, Indira Devi, Bhagavatula
Format: Article
Language:English
Subjects:
Adult
Anesthesia - methods
Anesthesiology
Clinical Report
Critical Care Medicine
Decompression, Surgical
Diagnosis
Emergency Medicine
Equipment and supplies
Female
Fiber optics
Foramen Magnum - surgery
Glycosaminoglycans
Humans
Intensive
Lung - physiopathology
Medicine
Medicine & Public Health
Mucopolysaccharidosis
Mucopolysaccharidosis IV - complications
Mucopolysaccharidosis IV - physiopathology
Pain Medicine
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Description
Summary:Morquio syndrome is a hereditary mucopolysaccharide disorder presenting with an abnormality of the craniocervical junction from childhood. We describe an adult patient who presented with Morquio syndrome who had subglottic narrowing of the airway, restrictive pulmonary disease, and mild mitral regurgitation and trivial aortic regurgitation. The anesthetic management of this patient for atlantoaxial stabilization is presented.
ISSN:0913-8668
1438-8359
DOI:10.1007/s00540-010-0963-9