Hereditary angioneurotic oedema

HAE is transmitted by an autosomal dominant gene. It is due to a defect in the complement system and should be distinguished from the other two types of angio-oedema, i.e. allergic and idiopathic types. Pathogenesis and treatment are discussed and two new cases of HAE have been reported here. I woul...

Full description

Saved in:
Bibliographic Details
Published in:Journal of laryngology and otology 1980-09, Vol.94 (9), p.1075-1079
Main Author: El-Ghazali, A. M. S.
Format: Article
Language:English
Subjects:
Adult
Airway Obstruction - prevention & control
Angioedema - drug therapy
Angioedema - genetics
Angioedema - immunology
Antifibrinolytic Agents - therapeutic use
Clinical records
Complement C1 Inactivator Proteins - blood
Danazol - therapeutic use
Female
Humans
Male
Middle Aged
Citations: Items that this one cites
Items that cite this one
Online Access:Get full text
Tags: Add Tag
No Tags, Be the first to tag this record!
Description
Summary:HAE is transmitted by an autosomal dominant gene. It is due to a defect in the complement system and should be distinguished from the other two types of angio-oedema, i.e. allergic and idiopathic types. Pathogenesis and treatment are discussed and two new cases of HAE have been reported here. I would stress here two points: first, that the family should be investigated for the possibility of HAE; secondly, that the patient should carry a medical card similar to those carried by haemophilic patients, containing the diagnosis, name of the G.P. and emergency treatment.
ISSN:0022-2151
1748-5460
DOI:10.1017/S0022215100089866