Electrophysiologic Studies in an Infant With Möbius Syndrome

The electrophysiologic findings in an infant with congenital facial diplegia (Möbius syndrome) are presented. As to serial electrically elicited blink reflexes, the R 1 amplitude was significantly reduced and the R2 latency was significantly prolonged. The M response of the orbicularis oculi muscle...

Full description

Saved in:
Bibliographic Details
Published in:Journal of child neurology 1993-04, Vol.8 (2), p.182-185
Main Authors: Hatanaka, Takeshi, Yoshijima, Satoshi, Hayashi, Nobana, Owa, Kenji, Suehiro, Yutaka, Shinomiya, Keisuke
Format: Article
Language:English
Subjects:
Blinking - physiology
Brain Stem - physiopathology
Dominance, Cerebral - physiology
Facial Nerve - physiopathology
Facial Paralysis - physiopathology
Female
Follow-Up Studies
Humans
Infant
Infant, Newborn
Median Nerve - physiopathology
Motor Neurons - physiology
Reaction Time - physiology
Synaptic Transmission - physiology
Tibial Nerve - physiopathology
Citations: Items that this one cites
Items that cite this one
Online Access:Get full text
Tags: Add Tag
No Tags, Be the first to tag this record!
Description
Summary:The electrophysiologic findings in an infant with congenital facial diplegia (Möbius syndrome) are presented. As to serial electrically elicited blink reflexes, the R 1 amplitude was significantly reduced and the R2 latency was significantly prolonged. The M response of the orbicularis oculi muscle showed slightly reduced amplitude. Auditory brainstem responses exhibited a prolonged time between waves I and V and reduced amplitude of wave V on the right side. Somatosensory evoked potentials and visual evoked potentials were normal. These findings suggest some degree of impairment of the peripheral facial nerve, and brainstem dysfunction including the pons and lateral medulla. (J Child Neurol 1983;8:182-185).
ISSN:0883-0738
1708-8283
DOI:10.1177/088307389300800213