Neurofibroma of the supraglottic larynx in childhood

The case of a male child with a benign neurogenic laryngeal tumour caused by von Recklinghausen's disease is presented. At the age of eight years, tracheostomy was necessary. The tumour, deforming the right half of the larynx and extending into the right half of the neck, was removed three year...

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Bibliographic Details
Published in:Journal of laryngology and otology 1994-02, Vol.108 (2), p.156-158
Main Authors: Czigner, Jenö, Fekete-Szabó, Gabriella
Format: Article
Language:English
Subjects:
Biological and medical sciences
Child
Clinical Records
Follow-Up Studies
Humans
Laryngeal neoplasms
Laryngeal Neoplasms - surgery
Male
Medical sciences
Neurofibromatosis
Neurofibromatosis 1 - pathology
Neurofibromatosis 1 - surgery
Non tumoral diseases
Otorhinolaryngology. Stomatology
Pedigree
Surgery
Tracheostomy
Upper respiratory tract, upper alimentary tract, paranasal sinuses, salivary glands: diseases, semeiology
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Summary:The case of a male child with a benign neurogenic laryngeal tumour caused by von Recklinghausen's disease is presented. At the age of eight years, tracheostomy was necessary. The tumour, deforming the right half of the larynx and extending into the right half of the neck, was removed three years later. Following this procedure, decannulation was possible, and the patient has been free of laryngological complaints for six years. Attention is drawn to the fact that autosomal dominantly inherited neurofibromatosis is a generalized benign tumour with a special form. If it involves any vital structure or forms a functional obstacle, meticulous surgical removal is necessary, and this provides good prospects over a long period.
ISSN:0022-2151
1748-5460
DOI:10.1017/S0022215100126155