Arthropathy associated with factor XIII deficiency

A 47‐year‐old man with congenital factor XIII deficiency developed recurrent hemarthrosis of the right ankle. He had radiologic evidence of permanent joint damage. A review of the literature revealed that hemarthrosis is not a rare manifestation of factor XIII deficiency; however, destructive change...

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Bibliographic Details
Published in:Arthritis and rheumatism 1986-06, Vol.29 (6), p.808-811
Main Authors: Thakker, Suman, McGehee, William, Quismorio, Francisco P.
Format: Article
Language:English
Subjects:
Ankle Joint - diagnostic imaging
Biological and medical sciences
Blood Transfusion
Factor XIII Deficiency - complications
Hemarthrosis - diagnostic imaging
Hemarthrosis - etiology
Hemarthrosis - therapy
Hematologic and hematopoietic diseases
Humans
Male
Medical sciences
Middle Aged
Plasma
Platelet diseases and coagulopathies
Radiography
Recurrence
Solubility
Urea
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Description
Summary:A 47‐year‐old man with congenital factor XIII deficiency developed recurrent hemarthrosis of the right ankle. He had radiologic evidence of permanent joint damage. A review of the literature revealed that hemarthrosis is not a rare manifestation of factor XIII deficiency; however, destructive changes in the joints are relatively uncommon in this disorder, in contrast with those changes seen in patients with classic hemophilia and arthropathy. The bleeding manifestations of factor XIII deficiency are readily correctable by plasma or cryoprecipitate infusions; this may account for the preservation of joint function and structure.
ISSN:0004-3591
1529-0131
DOI:10.1002/art.1780290617