Tetralogy of Fallot with absent ductus arteriosus and absent collateral pulmonary circulation: diagnostic and surgical implications during the neonatal period

A newborn infant with tetralogy of Fallot and presumed agenesis of the ductus arteriosus presented without the expected associated pulmonic regurgitation and aneurysmal pulmonary arteries. The presumption of agenesis of the ductus arteriosus was made because there was no reduction in cyanosis follow...

Full description

Saved in:
Bibliographic Details
Published in:Pediatric cardiology 1988-01, Vol.9 (1), p.45-49
Main Authors: Pahl, E, Muster, A J, Ilbawi, M N, DeLeon, S Y
Format: Article
Language:English
Subjects:
Collateral Circulation
Ductus Arteriosus - abnormalities
Ductus Arteriosus - diagnostic imaging
Humans
Infant, Newborn
Lung - abnormalities
Lung - diagnostic imaging
Lung - surgery
Male
Palliative Care - methods
Pulmonary Circulation
Radiography
Tetralogy of Fallot - diagnostic imaging
Tetralogy of Fallot - surgery
Citations: Items that this one cites
Items that cite this one
Online Access:Get full text
Tags: Add Tag
No Tags, Be the first to tag this record!
Description
Summary:A newborn infant with tetralogy of Fallot and presumed agenesis of the ductus arteriosus presented without the expected associated pulmonic regurgitation and aneurysmal pulmonary arteries. The presumption of agenesis of the ductus arteriosus was made because there was no reduction in cyanosis following prostaglandin E1 treatment and no remnant of ductus arteriosus could be demonstrated by angiography at 19 h of age. The fetal hemodynamics inferred in this infant are discussed with reference to the absence of aneurysmal pulmonary arteries. Closed transventricular pulmonary valvulotomy is recommended as emergency palliation for symptomatic newborns with this variant of tetralogy of Fallot because further reduction of pulmonary vascular bed, even temporarily, as in unilateral pulmonary artery cross-clamping for systemic-pulmonary anastomosis, may not be tolerated without the use of cardiopulmonary bypass.
ISSN:0172-0643
1432-1971
DOI:10.1007/BF02279884