Malformation and Stenosis of the Cricoid Cartilage in Association With Larsen's Syndrome

Three patients with the typical features of Larsen's syndrome are described. All three developed severe respiratory symptoms caused by a congenital subglottic stenosis. Tracheotomy and treatment of the stenosis by means of laryngotracheoplasty resulted in complete collapse of the cricoid cartil...

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Bibliographic Details
Published in:The Laryngoscope 1997-06, Vol.107 (6), p.792-794
Main Authors: Hoeve, Hans J., Joosten, Koen F.M., Bogers, J.J.C., Hazebroek, Frans W.J., Pfenninger, Jürg, van der Voort, Edwin, Leijala, Mauri
Format: Article
Language:English
Subjects:
Abnormalities, Multiple
Airway Obstruction - etiology
Anastomosis, Surgical
Biological and medical sciences
Constriction, Pathologic
Cricoid Cartilage - abnormalities
Cricoid Cartilage - pathology
Cricoid Cartilage - surgery
Facies
Female
Head and neck surgery. Maxillofacial surgery. Dental surgery. Orthodontics
Humans
Infant
Joint Dislocations - complications
Laryngostenosis - complications
Laryngostenosis - congenital
Laryngostenosis - surgery
Male
Medical sciences
Surgery (general aspects). Transplantations, organ and tissue grafts. Graft diseases
Surgery of the upper aerodigestive tract
Syndrome
Trachea - surgery
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Summary:Three patients with the typical features of Larsen's syndrome are described. All three developed severe respiratory symptoms caused by a congenital subglottic stenosis. Tracheotomy and treatment of the stenosis by means of laryngotracheoplasty resulted in complete collapse of the cricoid cartilage and the proximal tracheal skeleton. Lack of rigidity of the laryngeal and tracheal cartilages in patients with Larsen's syndrome could well be responsible for this failure. Surgical treatment consisted of resection of the stenotic and collapsed areas and end‐to‐end anastomosis. This therapy was eventually successful in all three patients.
ISSN:0023-852X
1531-4995
DOI:10.1097/00005537-199706000-00013