Fibrosarcoma in Children: A Rare Tumour with Long-Term Survival even with Advanced Disease A Report of 3 Cases

Fibrosarcoma is a rare tumour in children. The potential of malignancy has been questioned. We present three cases of fibrosarcoma in children. The follow-up periods range from 10 to 37 years. The first patient had pulmonary metastases at the time of diagnosis in 1958. The primary tumour in fossa is...

Full description

Saved in:
Bibliographic Details
Published in:Acta oncologica 1997, Vol.36 (4), p.438-440
Main Authors: Lilleng, Peer K., Monge, Odd R., Walløe, Anders, Trovik, Clement S., Hordvik, Markus, Høie, Johan, Dahl, Olav, Bang, Gisle
Format: Article
Language:English
Subjects:
Abdominal Neoplasms - pathology
Abdominal Neoplasms - surgery
Adolescent
Biological and medical sciences
Child, Preschool
Disease-Free Survival
Fibrosarcoma - pathology
Fibrosarcoma - secondary
Fibrosarcoma - surgery
Follow-Up Studies
Humans
Infant
Lung Neoplasms - secondary
Lung Neoplasms - surgery
Male
Mandibular Neoplasms - pathology
Mediastinal Neoplasms - secondary
Medical sciences
Mitosis
Multiple tumors. Solid tumors. Tumors in childhood (general aspects)
Muscle Neoplasms - pathology
Neoplasm Recurrence, Local - pathology
Survival Rate
Tumors
Vimentin - analysis
Citations: Items that this one cites
Items that cite this one
Online Access:Get full text
Tags: Add Tag
No Tags, Be the first to tag this record!
Description
Summary:Fibrosarcoma is a rare tumour in children. The potential of malignancy has been questioned. We present three cases of fibrosarcoma in children. The follow-up periods range from 10 to 37 years. The first patient had pulmonary metastases at the time of diagnosis in 1958. The primary tumour in fossa ischio-rectalis was resected in 1960. Lung metastases were resected in 1960 and 1989. Radiotherapy was given in 1992. He is still alive with metastases 37 years after the first manifestation of disease. The second patient had a primary tumour and several local recurrences in the mandible. He is alive without evidence of disease 4 years after resection of pulmonary metastases and 21 years after resection of the primary tumour. The third patient has no signs of recurrence or metastasic spread 10 years after a wide excision of subcutanous tumours of the left upper arm. The cases demonstrate a special tumour-entity of low-grade malignancy, which show a good prognosis and a wide spectrum of biological behaviour.
ISSN:0284-186X
1651-226X
DOI:10.3109/02841869709001294