Angiographic and morphologic features of the left ventricle in Ebstein's malformation

• Published in: The American journal of cardiology 1997-10, Vol.80 (8), p.1051-1059
• Main Authors: Daliento, Luciano, Angelini, Annalisa, Ho, Siew Yen, Frescura, Carla, Turrini, Pietro, Baratella, Maria Cristina, Thiene, Gaetano, Anderson, Robert H.
• Format: Article
• Language: English
• Subjects: Adolescent; Adult; Biological and medical sciences; Cardiovascular system; Child; Child, Preschool; Cineangiography; Coronary Angiography; Ebstein Anomaly - diagnostic imaging; Ebstein Anomaly - pathology; Female; Heart Ventricles - diagnostic imaging; Humans; Investigative techniques, diagnostic techniques (general aspects); Male; Medical sciences; Middle Aged; Pathology. Cytology. Biochemistry. Spectrometry. Miscellaneous investigative techniques; Retrospective Studies; Ventricular Dysfunction, Left - diagnostic imaging; Ventricular Dysfunction, Left - pathology
• ISSN: 0002-9149; 1879-1913
• DOI: 10.1016/S0002-9149(97)00602-4

Quantitative and qualitative cineangiographic analysis of the left ventricle (LV) was performed in 26 patients with isolated Ebstein's malformation, having a mean age of 23 ± 17 years. Nine autopsied hearts with isolated Ebstein's malformation were submitted to morphologic and morphometric analysis. In 4 of the cases, it was possible to make a direct correlation between the angiographic data obtained during life and the autopsy findings. On the basis of the LV end-diastolic volume we identified 3 groups of patients: 7 with volume 80 ml/m 2. The LV ejection fraction was reduced in 2 patients with normal LV enddiastolic volume and in 6 with increased LV end-diastolic volume. The ratio of ventricular mass to LV end-diastolic volume was always adequate, but a reduction of the ventricular contractive performance (end-systolic pressure to end-systolic volume ratio