Nosologic classification of Fazio-Londe disease

The observation of a progressive bulbar paralysis with lethal exit in a 20 years old patient, whose mother had died in the age of 29 years after a similar course of disease, is coordinated as Fazio: Londe-disease. But peculiarities are mentioned, that refer to traits of the special form of progressi...

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Bibliographic Details
Published in:Psychiatrie, Neurologie, und medizinische Psychologie Neurologie, und medizinische Psychologie, 1989-10, Vol.41 (10), p.596-604
Main Authors: Schulze, H A, Zschenderlein, R, Engel, E, Jänisch, W, Planitzer, J
Format: Article
Language:ger
Subjects:
Adult
Brain - pathology
Bulbar Palsy, Progressive - classification
Bulbar Palsy, Progressive - genetics
Bulbar Palsy, Progressive - pathology
Diagnosis, Differential
Humans
Male
Muscles - pathology
Spinal Cord - pathology
Syndrome
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Summary:The observation of a progressive bulbar paralysis with lethal exit in a 20 years old patient, whose mother had died in the age of 29 years after a similar course of disease, is coordinated as Fazio: Londe-disease. But peculiarities are mentioned, that refer to traits of the special form of progressive bulbar paralysis described by Kennedy and of Kugelberg-Welander-disease. A genetic basis of variability is supposed.
ISSN:0033-2739