VATS resection of an oesophageal leiomyoma in a patient with neurofibromatosis Recklinghausen

A series of reports in the literature suggest an association of neurofibromatosis Recklinghausen with intestinal tumors as carcinoids, leiomyomas and leiomyosarcomas. We present a case of a 23-year-old man with severe cutaneous manifestation of neurofibromatosis. Dysphagia was the mains ymptom. CT s...

Full description

Saved in:
Bibliographic Details
Published in:European journal of cardio-thoracic surgery 1997-10, Vol.12 (4), p.659-662
Main Authors: SCHMID, R. A, SCHÖB, O. M, KLOTZ, H.-P, VOGT, P, WEDER, W
Format: Article
Language:English
Subjects:
Adult
Biological and medical sciences
Endoscopy - methods
Esophageal Neoplasms - surgery
Humans
Leiomyoma - surgery
Male
Medical sciences
Neurofibromatosis 1 - surgery
Neurology
Thoracoscopy
Tumors of the nervous system. Phacomatoses
Videotape Recording
Citations: Items that this one cites
Items that cite this one
Online Access:Get full text
Tags: Add Tag
No Tags, Be the first to tag this record!
Description
Summary:A series of reports in the literature suggest an association of neurofibromatosis Recklinghausen with intestinal tumors as carcinoids, leiomyomas and leiomyosarcomas. We present a case of a 23-year-old man with severe cutaneous manifestation of neurofibromatosis. Dysphagia was the mains ymptom. CT scan suggested the diagnosis of an oesophageal leiomyoma. Theoesophageal muscle layers were split and the tumor was enucleated by video assisted thoracoscopic surgery (VATS). The postoperative course was uneventful. The patient was drinking liquids from day 1 and was eating anormal diet from day 3 postoperatively. He was dismissed from the hospital on the 4th postoperative day. We conclude that in patients with neurofibromatosis and oesophageal symptoms an intestinal manifestation of the disease in the oesophagus has to be considered and that VATS resection of intramural and extrinsic oesophageal leiomyomas is the treatment of choice.
ISSN:1010-7940
1873-734X
DOI:10.1016/S1010-7940(97)00210-8