Recurrent Pseudomonas bronchopneumonia and other symptoms as in cystic fibrosis in a child with type I pseudohypoaldosteronism

We report a child with multiple target organ pseudohypoaldosteronism type 1 with frequent recurrent pulmonary infections caused by Pseudomonas aeruginosa and Pasteurella multocida and high levels of chloride in sweat, urine and nasal secretion. Repetitive faecal chymotrypsin samples have all shown p...

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Bibliographic Details
Published in:Acta Paediatrica 1998-04, Vol.87 (4), p.472-474
Main Authors: Marthinsen, L, Kornfält, R, Aili, M, Andersson, D, Westgren, U, Schaedel, C
Format: Article
Language:English
Subjects:
Adrenals. Adrenal axis. Renin-angiotensin system (diseases)
Biological and medical sciences
Bronchopneumonia - complications
Bronchopneumonia - diagnosis
Bronchopneumonia - microbiology
Child
Chymotrypsin
cystic fibrosis
Cystic Fibrosis - diagnosis
Diagnosis, Differential
Endocrinopathies
Humans
Male
Medical sciences
Non tumoral diseases. Target tissue resistance. Benign neoplasms
Pneumonia, Bacterial - complications
pseudohypoaldosteronism
Pseudohypoaldosteronism - complications
Pseudomonas
Pseudomonas Infections - complications
Recurrence
respiratory infections
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Summary:We report a child with multiple target organ pseudohypoaldosteronism type 1 with frequent recurrent pulmonary infections caused by Pseudomonas aeruginosa and Pasteurella multocida and high levels of chloride in sweat, urine and nasal secretion. Repetitive faecal chymotrypsin samples have all shown pathological values in spite of no other sign of exocrine pancreas dysfunction. The similarities with cystic fibrosis and the importance of the salt content in bronchial fluid are discussed.
ISSN:0803-5253
1651-2227
DOI:10.1111/j.1651-2227.1998.tb01483.x