Unilateral pulmonary vein atresia: clinical and radiographic spectrum

Three cases of unilateral pulmonary vein atresia are presented to illustrate part of the clinical and radiographic spectrum of this anomaly. One patient had major associated cardiovascular abnormalities and pulmonary hypertension, one had recurrent hemoptysis, and the other patient was asymptomatic...

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Bibliographic Details
Published in:Pediatric cardiology 1983-04, Vol.4 (2), p.105-112
Main Authors: Beerman, L B, Oh, K S, Park, S C, Freed, M D, Sondheimer, H M, Fricker, F J, Mathews, R A, Fischer, D R
Format: Article
Language:English
Subjects:
Abnormalities, Multiple - diagnosis
Abnormalities, Multiple - physiopathology
Adolescent
Angiography
Collateral Circulation
Female
Humans
Lung - blood supply
Pulmonary Valve - abnormalities
Pulmonary Valve Stenosis - congenital
Pulmonary Valve Stenosis - diagnosis
Pulmonary Veins - abnormalities
Pulmonary Veins - diagnostic imaging
Radionuclide Imaging
Tomography, X-Ray Computed
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Summary:Three cases of unilateral pulmonary vein atresia are presented to illustrate part of the clinical and radiographic spectrum of this anomaly. One patient had major associated cardiovascular abnormalities and pulmonary hypertension, one had recurrent hemoptysis, and the other patient was asymptomatic with normal pulmonary artery pressure and no associated abnormalities. In one case, serial catheterizations indicated that the pulmonary vein atresia was acquired. This report stresses the radiographic, hemodynamic, and angiographic findings in patients with unilateral severe pulmonary venous obstruction. The embryology, pathology, and surgical approach are also discussed. The diagnosis should be strongly suspected before cardiac catheterization when typical features are present on the chest radiograph and isotopic ventilation perfusion scan.
ISSN:0172-0643
1432-1971
DOI:10.1007/bf02076334