Atrial paralysis due to progression of cardiac disease in a patient with Emery-Dreifuss muscular dystrophy

We present the progressive nature of the disease in a 26 year-old woman who had suffered from Emery-Dreifuss muscular dystrophy detected at the age of three. In 2002, at the age of 20, due to recurring presyncopal states accompanied by sinus bradycardia and atrioventricular block, she was implanted...

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Bibliographic Details
Published in:Cardiology journal 2011, Vol.18 (2), p.189-193
Main Authors: Wożakowska-Kapłon, Beata, Bąkowski, Dawid
Format: Article
Language:English
Subjects:
Adult
Atrioventricular Block - diagnosis
Atrioventricular Block - etiology
Atrioventricular Block - therapy
Bradycardia - diagnosis
Bradycardia - etiology
Bradycardia - therapy
Cardiac Pacing, Artificial - methods
Disease Progression
Electrocardiography
Female
Heart Atria
Humans
Muscular dystrophy
Muscular Dystrophy, Emery-Dreifuss - complications
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Summary:We present the progressive nature of the disease in a 26 year-old woman who had suffered from Emery-Dreifuss muscular dystrophy detected at the age of three. In 2002, at the age of 20, due to recurring presyncopal states accompanied by sinus bradycardia and atrioventricular block, she was implanted with a dual chamber pacing system. During testing of the pacing in 2008, permanent electrical atrial stand-still without atria stimulation were detected and the mode of heart stimulation was changed to VVIR.
ISSN:1897-5593
1897-5593
1898-018X